Orphanet Rare Disease Ontology

Last uploaded: July 3, 2024
Preferred Name

Extracutaneous mastocytoma
Synonyms
Definitions

A rare neoplastic disease characterized by a localized, unifocal, low-grade tumor composed of mature mast cells, without evidence of systemic mastocytosis or skin lesions. The tumor most commonly arises in the lung and shows a non-destructive growth pattern.

ID

http://www.orpha.net/ORDO/Orphanet_66662

definition

A rare neoplastic disease characterized by a localized, unifocal, low-grade tumor composed of mature mast cells, without evidence of systemic mastocytosis or skin lesions. The tumor most commonly arises in the lung and shows a non-destructive growth pattern.

definition_citation

Orphanet

expertlink

https://www.orpha.net/consor/cgi-bin/OC_Exp.php?Lng=en&Expert=66662

hasDbXref

ICD-10:C96.2

ICD-11:2A21.3

UMLS:C0272202

label

Extracutaneous mastocytoma

notation

ORPHA:66662

part_of

http://www.orpha.net/ORDO/Orphanet_98292

prefixIRI

ORDO:Orphanet_66662

prefLabel

Extracutaneous mastocytoma

treeView

http://www.orpha.net/ORDO/Orphanet_98292

subClassOf

http://www.orpha.net/ORDO/Orphanet_377788

http://www.orpha.net/ORDO/Orphanet_557493

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