Orphanet Rare Disease Ontology

Last uploaded: July 3, 2024
Preferred Name

Chronic intestinal pseudoobstruction

Synonyms

CIPO

Definitions

A rare and heterogeneous gastroenterological clinical syndrome characterized by recurrent symptoms of intestinal obstruction with radiological features of dilated small or large intestine in absence of any mechanical occlusive lesion. Permanent alterations in neural, muscular, or mesenchymal structures of the intestinal wall or its extrinsic neural control, chronically impair tonic and propulsive motor functions in one or more segments of the gut.

ID

http://www.orpha.net/ORDO/Orphanet_2978

alternative_term

CIPO

definition

A rare and heterogeneous gastroenterological clinical syndrome characterized by recurrent symptoms of intestinal obstruction with radiological features of dilated small or large intestine in absence of any mechanical occlusive lesion. Permanent alterations in neural, muscular, or mesenchymal structures of the intestinal wall or its extrinsic neural control, chronically impair tonic and propulsive motor functions in one or more segments of the gut.

definition_citation

Orphanet

expertlink

https://www.orpha.net/consor/cgi-bin/OC_Exp.php?Lng=en&Expert=2978

has_age_of_onset

All ages

hasDbXref

OMIM:609629

ICD-11:DA90.2

UMLS:C0238062

OMIM:300048

ICD-10:K59.8

OMIM:243180

OMIM:601223

label

Chronic intestinal pseudoobstruction

notation

ORPHA:2978

part_of

http://www.orpha.net/ORDO/Orphanet_104009

prefixIRI

ORDO:Orphanet_2978

prefLabel

Chronic intestinal pseudoobstruction

present_in

Worldwide AND has_point_prevalence_range : Unknown

treeView

http://www.orpha.net/ORDO/Orphanet_104009

subClassOf

http://www.orpha.net/ORDO/Orphanet_557493

http://www.orpha.net/ORDO/Orphanet_377792

Delete Subject Author Type Created
No notes to display