Preferred Name | Generalized pustular psoriasis | |
Synonyms |
GPP |
|
Definitions |
Generalized pustular psoriasis is a severe inflammatory skin disease that can be life-threatening and that is characterized by recurrent episodes of high fever, fatigue, episodic erythematous cutaneous eruptions with sterile cutaneous pustules formation on various parts of the body, and neutrophil leukocytosis. |
|
ID |
http://www.orpha.net/ORDO/Orphanet_247353 |
|
alternative_term |
GPP |
|
definition |
Generalized pustular psoriasis is a severe inflammatory skin disease that can be life-threatening and that is characterized by recurrent episodes of high fever, fatigue, episodic erythematous cutaneous eruptions with sterile cutaneous pustules formation on various parts of the body, and neutrophil leukocytosis. |
|
definition_citation |
Orphanet |
|
expertlink |
https://www.orpha.net/consor/cgi-bin/OC_Exp.php?Lng=en&Expert=247353 |
|
has_age_of_onset |
Adult |
|
has_inheritance |
Not applicable Autosomal recessive |
|
hasDbXref |
OMIM:614204 UMLS:C0343055 ICD-11:EA90.40 ICD-10:L40.1 OMIM:616106 |
|
label |
Generalized pustular psoriasis |
|
notation |
ORPHA:247353 |
|
part_of | ||
prefixIRI |
ORDO:Orphanet_247353 |
|
prefLabel |
Generalized pustular psoriasis |
|
present_in |
France AND has_point_prevalence_average_value : 0.18 AND has_point_prevalence_range : 1-9 / 1 000 000 Europe AND has_point_prevalence_range : 1-9 / 1 000 000 |
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treeView | ||
subClassOf |