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Orphanet Rare Disease Ontology
Last uploaded:
July 3, 2024
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| Preferred Name | Kaposiform hemangioendothelioma | |
| Synonyms |
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| Definitions |
A rare low-grade malignant cutaneous or visceral vascular tumour that may be associated with severe thrombopaenia with consumption coagulopathy (Kasabach-Merritt syndrome) in pediatric patients. |
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| ID |
http://www.orpha.net/ORDO/Orphanet_2122 |
|
| definition |
A rare low-grade malignant cutaneous or visceral vascular tumour that may be associated with severe thrombopaenia with consumption coagulopathy (Kasabach-Merritt syndrome) in pediatric patients.
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| definition_citation |
Orphanet
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| expertlink |
https://www.orpha.net/consor/cgi-bin/OC_Exp.php?Lng=en&Expert=2122 |
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| has_age_of_onset |
All ages
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| has_inheritance |
Not applicable
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| hasDbXref |
ICD-11:XH6PA4 ICD-10:C49.9 MeSH:C537007 UMLS:C1367420 ICD-11:2F72.Y
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| label |
Kaposiform hemangioendothelioma
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| notation |
ORPHA:2122
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| part_of | ||
| prefixIRI |
ORDO:Orphanet_2122
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| prefLabel |
Kaposiform hemangioendothelioma
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| present_in |
Worldwide AND has_point_prevalence_range : Unknown
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| treeView | ||
| subClassOf |
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