loading...| Preferred Name | Multicentric reticulohistiocytosis | |
| Synonyms |
Giant cell histiocytomatosis Lipoid dermatoarthritis |
|
| Definitions |
A rare non-Langerhans cell histiocytosis characterized by the association of specific nodular skin lesions and destructive arthritis. |
|
| ID |
http://www.orpha.net/ORDO/Orphanet_139436 |
|
| alternative_term |
Giant cell histiocytomatosis Lipoid dermatoarthritis |
|
| definition |
A rare non-Langerhans cell histiocytosis characterized by the association of specific nodular skin lesions and destructive arthritis. |
|
| definition_citation |
Orphanet |
|
| expertlink |
https://www.orpha.net/consor/cgi-bin/OC_Exp.php?Lng=en&Expert=139436 |
|
| has_age_of_onset |
Adult |
|
| has_inheritance |
Not applicable |
|
| hasDbXref |
MedDRA:10070595 UMLS:C0311284 ICD-10:D76.3 ICD-11:EE8Y |
|
| label |
Multicentric reticulohistiocytosis |
|
| notation |
ORPHA:139436 |
|
| part_of | ||
| prefixIRI |
ORDO:Orphanet_139436 |
|
| prefLabel |
Multicentric reticulohistiocytosis |
|
| present_in |
Worldwide AND has_cases/families_value : 200.0 (Case) Worldwide AND has_point_prevalence_range : Unknown |
|
| treeView | ||
| subClassOf |