Preferred Name

Infantile Spasms
Synonyms

Nodding Spasm

Lightning Attacks

West Syndrome

Salaam Seizures

Salaam Attacks

Jackknife Seizures

Spasmus Nutans

Hypsarrhythmia

Definitions

An epileptic syndrome characterized by the triad of infantile spasms, hypsarrhythmia, and arrest of psychomotor development at seizure onset. The majority present between 3-12 months of age, with spasms consisting of combinations of brief flexor or extensor movements of the head, trunk, and limbs. The condition is divided into two forms: cryptogenic (idiopathic) and symptomatic (secondary to a known disease process such as intrauterine infections; nervous system abnormalities; BRAIN DISEASES, METABOLIC, INBORN; prematurity; perinatal asphyxia; TUBEROUS SCLEROSIS; etc.) (MeSH).

ID

http://uri.neuinfo.org/nif/nifstd/birnlex_12744

alternative label

Nodding Spasm

Lightning Attacks

West Syndrome

Salaam Seizures

Salaam Attacks

Jackknife Seizures

Spasmus Nutans

Hypsarrhythmia

createdDate

2007-10-08

definingCitation

Menkes, Textbook of Child Neurology, 5th ed, pp744-8

definition

An epileptic syndrome characterized by the triad of infantile spasms, hypsarrhythmia, and arrest of psychomotor development at seizure onset. The majority present between 3-12 months of age, with spasms consisting of combinations of brief flexor or extensor movements of the head, trunk, and limbs. The condition is divided into two forms: cryptogenic (idiopathic) and symptomatic (secondary to a known disease process such as intrauterine infections; nervous system abnormalities; BRAIN DISEASES, METABOLIC, INBORN; prematurity; perinatal asphyxia; TUBEROUS SCLEROSIS; etc.) (MeSH).

editorial note

http://uri.neuinfo.org/nif/nifstd/readable/uncurated

externalSourceId

D013036

hasBirnlexCurator

http://uri.neuinfo.org/nif/nifstd/readable/Bill_Bug

hasCurationStatus

http://uri.neuinfo.org/nif/nifstd/readable/uncurated

hasDefinitionSource

http://uri.neuinfo.org/nif/nifstd/readable/MeSH_defSource

hasExternalSource

http://uri.neuinfo.org/nif/nifstd/readable/MeSH

label

Infantile Spasms

MeshUid

D013036

modifiedDate

2007-10-08

note

An epileptic syndrome characterized by the triad of infantile spasms, hypsarrhythmia, and arrest of psychomotor development at seizure onset. The majority present between 3-12 months of age, with spasms consisting of combinations of brief flexor or extensor movements of the head, trunk, and limbs. The condition is divided into two forms: cryptogenic (idiopathic) and symptomatic (secondary to a known disease process such as intrauterine infections; nervous system abnormalities; BRAIN DISEASES, METABOLIC, INBORN; prematurity; perinatal asphyxia; TUBEROUS SCLEROSIS; etc.) (MeSH).

http://uri.neuinfo.org/nif/nifstd/readable/uncurated

preferred label

Infantile Spasms

putativeClassExtension

Symptomatic West Syndrome

Cryptogenic West Syndrome

Symptomatic Infantile Spasms

Cryptogenic Infantile Spasms

Resource Identifier

D013036

synonym

Nodding Spasm

Lightning Attacks

West Syndrome

Salaam Seizures

Salaam Attacks

Jackknife Seizures

Spasmus Nutans

Hypsarrhythmia

usageNote

MeSH includes implied subtypes

subClassOf

http://purl.obolibrary.org/obo/DOID_1827

http://uri.neuinfo.org/nif/nifstd/birnlex_12737

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