Preferred Name

granulomatosis with polyangiitis

Synonyms

Wegener granulomatosis, formerly

Definitions

An autoimmune disease that is characterized by necrotizing granulomatous inflammation of the upper and lower respiratory tract, glomerulonephritis, vasculitis, and the presence of antineutrophil cytoplasmatic autoantibodies (ANCAs) in patient sera, and is located_in lung, located_in kidney, located_in skin resulting from an autoimmune attack by antineutrophil cytoplasmic antibodies against small and medium-size blood vessels.

ID

http://purl.obolibrary.org/obo/DOID_12132

database_cross_reference

UMLS_CUI:C3495801

ICD10CM:M31.3

ICD9CM:446.4

OMIM:608710

SNOMEDCT_US_2023_03_01:195353004

MESH:D014890

GARD:7880

NCI:C3444

definition

An autoimmune disease that is characterized by necrotizing granulomatous inflammation of the upper and lower respiratory tract, glomerulonephritis, vasculitis, and the presence of antineutrophil cytoplasmatic autoantibodies (ANCAs) in patient sera, and is located_in lung, located_in kidney, located_in skin resulting from an autoimmune attack by antineutrophil cytoplasmic antibodies against small and medium-size blood vessels.

disease has location

http://purl.obolibrary.org/obo/UBERON_0002048

http://purl.obolibrary.org/obo/UBERON_0000014

http://purl.obolibrary.org/obo/UBERON_0000178

http://purl.obolibrary.org/obo/UBERON_0002113

has exact synonym

Wegener granulomatosis, formerly

Necrotizing respiratory granulomatosis

has symptom

http://purl.obolibrary.org/obo/SYMP_0000153

http://purl.obolibrary.org/obo/SYMP_0000709

has_obo_namespace

disease_ontology

id

DOID:12132

in_subset

http://purl.obolibrary.org/obo/doid#NCIthesaurus

http://purl.obolibrary.org/obo/doid#DO_rare_slim

label

granulomatosis with polyangiitis

notation

DOID:12132

prefLabel

granulomatosis with polyangiitis

subClassOf

http://purl.obolibrary.org/obo/DOID_37

http://purl.obolibrary.org/obo/DOID_0060050

http://purl.obolibrary.org/obo/DOID_557

http://purl.obolibrary.org/obo/DOID_850

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Delete Mapping To Ontology Source
http://purl.obolibrary.org/obo/DOID_12132 DTO SAME_URI
http://purl.obolibrary.org/obo/DOID_12132 BAO SAME_URI
http://purl.obolibrary.org/obo/DOID_12132 EPIO SAME_URI
http://purl.obolibrary.org/obo/DOID_12132 HHEAR SAME_URI
http://purl.obolibrary.org/obo/DOID_12132 ODAE SAME_URI
http://purl.obolibrary.org/obo/DOID_12132 MIDO SAME_URI
http://purl.obolibrary.org/obo/DOID_12132 FNS-H SAME_URI
http://purl.obolibrary.org/obo/DOID_12132 DOID SAME_URI
http://purl.obolibrary.org/obo/MONDO_0012105 MONDO LOOM
http://nanbyodata.jp/ontology/NANDO_2200424 NANDO LOOM
http://nanbyodata.jp/ontology/NANDO_1200263 NANDO LOOM
http://www.ebi.ac.uk/efo/EFO_0005297 CCONT LOOM
http://www.ebi.ac.uk/efo/EFO_0005297 HSPO LOOM
http://purl.obolibrary.org/obo/OMIT_0015716 OMIT LOOM
http://purl.bioontology.org/ontology/MEDDRA/10072579 MEDDRA LOOM
http://purl.obolibrary.org/obo/NCIT_C3444 BERO LOOM
https://github.com/sap218/ocimido/blob/master/ontology/ocimido.owl#OCIMIDO_00065 OCIMIDO LOOM
http://www.orpha.net/ORDO/Orphanet_900 ORDO LOOM
http://www.semanticweb.org/admin/ontologies/2022/7/MIO:00704 MIO LOOM
http://id.nlm.nih.gov/mesh/D014890 MDM LOOM
http://purl.obolibrary.org/obo/DOID_12132 BAO LOOM
http://purl.obolibrary.org/obo/DOID_12132 EPIO LOOM
http://purl.obolibrary.org/obo/DOID_12132 HHEAR LOOM
http://purl.obolibrary.org/obo/DOID_12132 MIDO LOOM
http://purl.obolibrary.org/obo/DOID_12132 FNS-H LOOM
http://www.phoc.org.cn/pmo/class/PMO_00036421 PMAPP-PMO LOOM
http://purl.bioontology.org/ontology/SNOMEDCT/195353004 SNOMEDCT LOOM
http://purl.bioontology.org/ontology/MESH/D014890 MESH LOOM
http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C3444 NCIT LOOM
http://purl.jp/bio/4/id/201506042300718467 IOBC LOOM
http://purl.bioontology.org/ontology/OMIM/608710 OMIM LOOM
http://purl.obolibrary.org/obo/MONDO_0012105 DOVES LOOM
http://purl.obolibrary.org/obo/MONDO_0012105 KTAO LOOM
http://radlex.org/RID/RID3702 RADLEX LOOM
http://www.ebi.ac.uk/efo/EFO_0005297 EFO LOOM
http://purl.obolibrary.org/obo/DOID_12132 DOID LOOM