Preferred Name

Kasabach-Merritt Syndrome [Disease/Finding]

Synonyms

Hemangioma Thrombocytopenia Syndrome

ID

http://purl.bioontology.org/ontology/NDFRT/N0000183384

altLabel

Hemangioma Thrombocytopenia Syndrome

Thrombocytopenia-Hemangioma Syndrome

Kasabach-Merritt Syndrome

Kasabach-Merritt Phenomenon

Hemangioma-Thrombocytopenia Syndrome

cui

C0221025

MESH DEFINITION

Rapidly growing vascular lesion along the midline axis of the neck, upper trunk, and extremities that is characterized by CONSUMPTION COAGULOPATHY; THROMBOCYTOPENIA; and HEMOLYTIC ANEMIA. It is often associated with infantile Kaposiform HEMANGIOENDOTHELIOMA and other vascular tumors such as tufted ANGIOMA.

MESH DUI

D059885

MeSH name

Kasabach-Merritt Syndrome

MESH UI

M0551903

NDFRT kind

DISEASE_KIND

notation

N0000183384

NUI

N0000183384

prefLabel

Kasabach-Merritt Syndrome [Disease/Finding]

tui

T047

subClassOf

http://purl.bioontology.org/ontology/NDFRT/N0000001451

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