Preferred Name

Dermatofibrosarcoma [Disease/Finding]

Synonyms

Dermatofibrosarcoma

ID

http://purl.bioontology.org/ontology/NDFRT/N0000003697

altLabel

Dermatofibrosarcoma

Darier-Hoffmann Tumor

Dermatofibrosarcoma Protuberan

Darier-Ferrand Tumor

cui

C0206647

May be treated by

http://purl.bioontology.org/ontology/NDFRT/N0000166057

http://purl.bioontology.org/ontology/NDFRT/N0000148699

http://purl.bioontology.org/ontology/NDFRT/N0000148698

http://purl.bioontology.org/ontology/NDFRT/N0000166058

MESH DEFINITION

A sarcoma of the deep layers of the skin. The tumors are locally aggressive tends to recur but rarely metastatic. It can be classified into variants depending on the cell type tumors are derived from or by its characteristics: Pigmented variant from MELANIN-containing DERMAL DENDRITIC CELLS; Myxoid variant, myxoid STROMAL CELLS; Giant cell variant characterized by GIANT CELLS in the tumors; and Fibrosarcomatous variant chracterized by tumor areas histologically indistinguishable from FIBROSARCOMA.

MESH DUI

D018223

MeSH name

Dermatofibrosarcoma

MESH UI

M0027452

NDFRT kind

DISEASE_KIND

notation

N0000003697

NUI

N0000003697

prefLabel

Dermatofibrosarcoma [Disease/Finding]

SNOMED CID

76594008

tui

T191

subClassOf

http://purl.bioontology.org/ontology/NDFRT/N0000001248

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