Preferred Name |
Autoimmune Lymphoproliferative Syndrome |
|
Synonyms |
Autoimmune Lymphoproliferative Syndrome (ALPS) Autoimmune Lymphoproliferative Syndrome Canale-Smith Syndrome ALPS |
|
Definitions |
An autoimmune hematologic disorder characterized by autoimmune hemolytic anemia, thrombocytopenia, lymphadenopathy, hepatomegaly and splenomegaly. Patients are at an increased risk of developing Hodgkin and non-Hodgkin lymphomas. |
|
ID |
http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C37864 |
|
code |
C37864 |
|
Concept_In_Subset |
http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C157711 http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C116977 |
|
Contributing_Source |
CTRP GDC |
|
DEFINITION |
An autoimmune hematologic disorder characterized by autoimmune hemolytic anemia, thrombocytopenia, lymphadenopathy, hepatomegaly and splenomegaly. Patients are at an increased risk of developing Hodgkin and non-Hodgkin lymphomas. |
|
Display_Name |
Autoimmune Lymphoproliferative Syndrome |
|
FULL_SYN |
Autoimmune Lymphoproliferative Syndrome (ALPS) Autoimmune Lymphoproliferative Syndrome Canale-Smith Syndrome ALPS |
|
Is_Value_For_GDC_Property | ||
label |
Autoimmune Lymphoproliferative Syndrome |
|
Legacy Concept Name |
Autoimmune_Lymphoproliferative_Syndrome |
|
Maps_To |
Autoimmune Lymphoproliferative Syndrome (ALPS) |
|
Preferred_Name |
Autoimmune Lymphoproliferative Syndrome |
|
prefixIRI |
Thesaurus:C37864 |
|
Semantic_Type |
Disease or Syndrome |
|
UMLS_CUI |
C1328840 |
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subClassOf |