loading...| Preferred Name | Granulomatosis with Polyangiitis | |
| Synonyms |
Wegener Granulomatosis Granulomatosis with Polyangiitis Wegener's Granulomatosis GPA |
|
| Definitions |
A rare, autoimmune, systemic medium and small size vasculitis. It is characterized by the formation of necrotizing granulomas in the respiratory tract, necrotizing angiitis, and glomerulonephritis. |
|
| ID |
http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C3444 |
|
| ALT_DEFINITION |
Systemic vasculitis affecting small to medium-sized vessels, characterized by necrotizing granulomas in the respiratory tract, necrotizing angiitis, glomerulonephritis with little to no immune complex deposition, and typically positive for antineutrophil cytoplasmic antibody staining in a cytoplasmic pattern (C-ANCA; antiproteinase 3). |
|
| code |
C3444 |
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| Concept_In_Subset |
http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C118468 http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C90259 |
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| Contributing_Source |
Cellosaurus NICHD |
|
| DEFINITION |
A rare, autoimmune, systemic medium and small size vasculitis. It is characterized by the formation of necrotizing granulomas in the respiratory tract, necrotizing angiitis, and glomerulonephritis. |
|
| FULL_SYN |
Wegener Granulomatosis Granulomatosis with Polyangiitis Wegener's Granulomatosis GPA |
|
| label |
Granulomatosis with Polyangiitis |
|
| Legacy Concept Name |
Wegener_s_Granulomatosis |
|
| Preferred_Name |
Granulomatosis with Polyangiitis |
|
| prefixIRI |
Thesaurus:C3444 |
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| Semantic_Type |
Disease or Syndrome |
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| UMLS_CUI |
C3495801 |
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| subClassOf |
http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C26912 |