National Cancer Institute Thesaurus

Last uploaded: February 23, 2024
Preferred Name

Childhood Dermatomyositis

Synonyms

Juvenile Dermatomyositis

Childhood Dermatomyositis

JDM

Definitions

An inflammatory myopathy of childhood resulting in muscle weakness, and associated with a characteristic skin rash.

ID

http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C27576

ALT_DEFINITION

An inflammatory myopathy of childhood resulting in symmetric proximal muscle weakness, and associated with characteristic cutaneous findings, such as heliotrope rash or Gottron's papules.

code

C27576

Concept_In_Subset

http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C118468

http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C90259

http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C192842

http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C165258

http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C189762

http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C118464

Contributing_Source

Cellosaurus

MedDRA

NICHD

DEFINITION

An inflammatory myopathy of childhood resulting in muscle weakness, and associated with a characteristic skin rash.

FULL_SYN

Juvenile Dermatomyositis

Childhood Dermatomyositis

JDM

label

Childhood Dermatomyositis

Legacy Concept Name

Childhood_Dermatomyositis

Maps_To

Childhood dermatomyositis

Preferred_Name

Childhood Dermatomyositis

prefixIRI

Thesaurus:C27576

Semantic_Type

Disease or Syndrome

UMLS_CUI

C2931785

subClassOf

http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C26744

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