loading...| Preferred Name | primary progressive aphasia | |
| Synonyms |
primary progressive aphasia syndrome PPA Mesulam syndrome |
|
| Definitions |
Primary progressive aphasia (PPA) is a neurodegenerative disorder, characterized by a primary dissolution of language, with relative sparing of other mental faculties for at least the first 2 years of illness. PPA is recognized as the language variant in the frontotemporal dementia (FTD) spectrum of disorders. PPA can be classified into 3 subtypes based on specific speech and language features: semantic dementia (SD), progressive non-fluent aphasia (PNFA) and logopenic progressive aphasia (lv-PPA). |
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| ID |
http://purl.obolibrary.org/obo/MONDO_0019806 |
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| database_cross_reference |
MESH:D018888 EFO:0009053 Orphanet:95432 DOID:0081388 GARD:8541 MEDGEN:79466 NCIT:C85024 UMLS:C0282513 |
|
| definition |
Primary progressive aphasia (PPA) is a neurodegenerative disorder, characterized by a primary dissolution of language, with relative sparing of other mental faculties for at least the first 2 years of illness. PPA is recognized as the language variant in the frontotemporal dementia (FTD) spectrum of disorders. PPA can be classified into 3 subtypes based on specific speech and language features: semantic dementia (SD), progressive non-fluent aphasia (PNFA) and logopenic progressive aphasia (lv-PPA). |
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| has_exact_synonym |
PPA Mesulam syndrome |
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| has_related_synonym |
primary progressive aphasia syndrome |
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| IAO_0000233 | ||
| id |
MONDO:0019806 |
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| in_subset |
http://purl.obolibrary.org/obo/mondo/mondo-simple#otar http://purl.obolibrary.org/obo/mondo/mondo-simple#ordo_group_of_disorders http://purl.obolibrary.org/obo/mondo/mondo-simple#rare http://purl.obolibrary.org/obo/mondo/mondo-simple#disease_grouping |
|
| label |
primary progressive aphasia |
|
| notation |
MONDO:0019806 |
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| prefLabel |
primary progressive aphasia |
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| skos_exactMatch |
http://identifiers.org/medgen/79466 http://purl.obolibrary.org/obo/Orphanet_95432 http://purl.obolibrary.org/obo/EFO_0009053 http://purl.obolibrary.org/obo/DOID_0081388 http://linkedlifedata.com/resource/umls/id/C0282513 |
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| treeView | ||
| subClassOf |