loading...| Preferred Name |
primary biliary cholangitis |
|
| Synonyms |
Hanot syndrome primary biliary cirrhosis biliary liver cirrhosis primary Bilary cirrhosis (PBC) PBC chronic non-suppurative destructive cholangitis chronic nonsuppurative destructive cholangitis cholestatic cirrhosis familial primary biliary cirrhosis biliary cirrhosis, primary |
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| Definitions |
Primary biliary cholangitis (PBC) is a chronic and slowly progressive cholestatic liver disease of autoimmune etiology characterized by injury of the intrahepatic bile ducts that may eventually lead to liver failure. |
|
| ID |
http://purl.obolibrary.org/obo/MONDO_0005388 |
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| closeMatch | ||
| database_cross_reference |
MESH:D008105 SCTID:31712002 MedDRA:10004661 MedDRA:10019137 ICD9:571.6 UMLS:C0008312 icd11.foundation:649193479 OMIMPS:109720 NORD:1604 Orphanet:186 DOID:12236 EFO:1001486 GARD:7459 NCIT:C27167 |
|
| definition |
Primary biliary cholangitis (PBC) is a chronic and slowly progressive cholestatic liver disease of autoimmune etiology characterized by injury of the intrahepatic bile ducts that may eventually lead to liver failure. |
|
| exactMatch |
https://omim.org/phenotypicSeries/PS109720 http://purl.obolibrary.org/obo/DOID_12236 http://identifiers.org/snomedct/31712002 http://linkedlifedata.com/resource/umls/id/C0008312 http://purl.obolibrary.org/obo/NCIT_C27167 |
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| has_exact_synonym |
Hanot syndrome primary biliary cirrhosis biliary liver cirrhosis primary Bilary cirrhosis (PBC) PBC chronic non-suppurative destructive cholangitis chronic nonsuppurative destructive cholangitis cholestatic cirrhosis |
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| has_related_synonym |
familial primary biliary cirrhosis biliary cirrhosis, primary |
|
| id |
MONDO:0005388 |
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| in_subset |
http://purl.obolibrary.org/obo/mondo#ordo_disease http://purl.obolibrary.org/obo/mondo#rare http://purl.obolibrary.org/obo/mondo#nord_rare http://purl.obolibrary.org/obo/mondo#orphanet_rare |
|
| label |
primary biliary cholangitis |
|
| notation |
MONDO:0005388 |
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| prefLabel |
primary biliary cholangitis |
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| treeView | ||
| subClassOf |