Preferred Name |
paraganglioma |
|
Synonyms |
paragangliomas tumour of paraganglion tumor of the paraganglion neoplasm of paraganglion Paraganglionic tumour tumor of paraganglion tumour of the paraganglion paraganglion tumor paraganglion tumour neoplasm of the paraganglion paraganglion neoplasm Paraganglionic neoplasm paraganglioma Paraganglionic tumor chemodectoma |
|
Definitions |
A benign or malignant neoplasm arising from paraganglia located along the sympathetic or parasympathetic nerves. Infrequently, it may arise outside the usual distribution of the sympathetic and parasympathetic paraganglia. Tumors arising from the adrenal gland medulla are called pheochromocytomas. Morphologically, paragangliomas usually display a nesting (Zellballen) growth pattern. There are no reliable morphologic criteria to distinguish between benign and malignant paragangliomas. The only definitive indicator of malignancy is the presence of regional or distant metastases. |
|
ID |
http://purl.obolibrary.org/obo/MONDO_0000448 |
|
database_cross_reference |
OMIMPS:168000 NCIT:C3308 ICDO:8680/1 SCTID:127027008 DOID:0050773 ONCOTREE:PGNG ICD9:239.7 MESH:D010235 UMLS:C0030421 EFO:1000453 |
|
definition |
A benign or malignant neoplasm arising from paraganglia located along the sympathetic or parasympathetic nerves. Infrequently, it may arise outside the usual distribution of the sympathetic and parasympathetic paraganglia. Tumors arising from the adrenal gland medulla are called pheochromocytomas. Morphologically, paragangliomas usually display a nesting (Zellballen) growth pattern. There are no reliable morphologic criteria to distinguish between benign and malignant paragangliomas. The only definitive indicator of malignancy is the presence of regional or distant metastases. |
|
disease arises from structure | ||
exactMatch |
http://identifiers.org/snomedct/127027008 http://purl.obolibrary.org/obo/DOID_0050773 https://omim.org/phenotypicSeries/PS168000 http://linkedlifedata.com/resource/umls/id/C0030421 |
|
has_exact_synonym |
paragangliomas tumour of paraganglion tumor of the paraganglion neoplasm of paraganglion Paraganglionic tumour tumor of paraganglion tumour of the paraganglion paraganglion tumor paraganglion tumour neoplasm of the paraganglion paraganglion neoplasm Paraganglionic neoplasm paraganglioma Paraganglionic tumor |
|
has_narrow_synonym |
chemodectoma |
|
IAO_0000233 | ||
id |
MONDO:0000448 |
|
in_subset |
http://purl.obolibrary.org/obo/mondo#rare |
|
label |
paraganglioma |
|
notation |
MONDO:0000448 |
|
prefLabel |
paraganglioma |
|
treeView |
http://purl.obolibrary.org/obo/MONDO_0021635 http://purl.obolibrary.org/obo/MONDO_0100545 |
|
subClassOf |
http://purl.obolibrary.org/obo/MONDO_0021635 http://purl.obolibrary.org/obo/MONDO_0100545 |