Mondo Disease Ontology

Last uploaded: May 9, 2024
Preferred Name

paraganglioma

Synonyms

paragangliomas

tumour of paraganglion

tumor of the paraganglion

neoplasm of paraganglion

Paraganglionic tumour

tumor of paraganglion

tumour of the paraganglion

paraganglion tumor

paraganglion tumour

neoplasm of the paraganglion

paraganglion neoplasm

Paraganglionic neoplasm

paraganglioma

Paraganglionic tumor

chemodectoma

Definitions

A benign or malignant neoplasm arising from paraganglia located along the sympathetic or parasympathetic nerves. Infrequently, it may arise outside the usual distribution of the sympathetic and parasympathetic paraganglia. Tumors arising from the adrenal gland medulla are called pheochromocytomas. Morphologically, paragangliomas usually display a nesting (Zellballen) growth pattern. There are no reliable morphologic criteria to distinguish between benign and malignant paragangliomas. The only definitive indicator of malignancy is the presence of regional or distant metastases.

ID

http://purl.obolibrary.org/obo/MONDO_0000448

database_cross_reference

OMIMPS:168000

NCIT:C3308

ICDO:8680/1

SCTID:127027008

DOID:0050773

ONCOTREE:PGNG

ICD9:239.7

MESH:D010235

UMLS:C0030421

EFO:1000453

definition

A benign or malignant neoplasm arising from paraganglia located along the sympathetic or parasympathetic nerves. Infrequently, it may arise outside the usual distribution of the sympathetic and parasympathetic paraganglia. Tumors arising from the adrenal gland medulla are called pheochromocytomas. Morphologically, paragangliomas usually display a nesting (Zellballen) growth pattern. There are no reliable morphologic criteria to distinguish between benign and malignant paragangliomas. The only definitive indicator of malignancy is the presence of regional or distant metastases.

disease arises from structure

http://purl.obolibrary.org/obo/CL_0011012

exactMatch

http://identifiers.org/snomedct/127027008

http://purl.obolibrary.org/obo/DOID_0050773

https://omim.org/phenotypicSeries/PS168000

http://linkedlifedata.com/resource/umls/id/C0030421

http://purl.obolibrary.org/obo/NCIT_C3308

http://identifiers.org/mesh/D010235

has_exact_synonym

paragangliomas

tumour of paraganglion

tumor of the paraganglion

neoplasm of paraganglion

Paraganglionic tumour

tumor of paraganglion

tumour of the paraganglion

paraganglion tumor

paraganglion tumour

neoplasm of the paraganglion

paraganglion neoplasm

Paraganglionic neoplasm

paraganglioma

Paraganglionic tumor

has_narrow_synonym

chemodectoma

IAO_0000233

https://github.com/monarch-initiative/mondo/issues/6877

id

MONDO:0000448

in_subset

http://purl.obolibrary.org/obo/mondo#rare

http://purl.obolibrary.org/obo/mondo#otar

http://purl.obolibrary.org/obo/mondo#inferred_rare

label

paraganglioma

notation

MONDO:0000448

prefLabel

paraganglioma

treeView

http://purl.obolibrary.org/obo/MONDO_0021635

http://purl.obolibrary.org/obo/MONDO_0100545

http://purl.obolibrary.org/obo/MONDO_0019496

http://purl.obolibrary.org/obo/MONDO_0002366

subClassOf

http://purl.obolibrary.org/obo/MONDO_0021635

http://purl.obolibrary.org/obo/MONDO_0100545

http://purl.obolibrary.org/obo/MONDO_0019496

http://purl.obolibrary.org/obo/MONDO_0002366

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Delete Mapping To Ontology Source
http://purl.obolibrary.org/obo/MONDO_0000448 OBA SAME_URI
http://purl.obolibrary.org/obo/MONDO_0000448 DOVES SAME_URI
http://www.ebi.ac.uk/efo/EFO_1000453 EFO LOOM
http://purl.obolibrary.org/obo/DOID_0050773 DOID LOOM
http://purl.obolibrary.org/obo/MONDO_0000448 OBA LOOM
http://purl.obolibrary.org/obo/MPATH_403 MPATH LOOM
http://www.gamuts.net/entity#paraganglioma GAMUTS LOOM
http://purl.bioontology.org/ontology/RCD/Xa99M RCD LOOM
http://phenomebrowser.net/ontologies/mesh/mesh.owl#C04.557.465.625.650.700 RH-MESH LOOM
http://purl.obolibrary.org/obo/MONDO_0000448 DOVES LOOM
http://www.semanticweb.org/ontologies/2012/11/abnormalities.owl#phenodb:2408 IFAR LOOM
http://radlex.org/RID/RID4512 RADLEX LOOM
http://doe-generated-ontology.com/OntoAD#C0030421 ONTOAD LOOM
http://purl.obolibrary.org/obo/DOID_0050773 DTO LOOM
http://purl.obolibrary.org/obo/DOID_0050773 BAO LOOM
http://purl.obolibrary.org/obo/DOID_0050773 HHEAR LOOM
http://purl.obolibrary.org/obo/DOID_0050773 NIFSTD LOOM
http://purl.obolibrary.org/obo/DOID_0050773 FNS-H LOOM
http://purl.bioontology.org/ontology/MEDDRA/10073860 MEDDRA LOOM
http://www.phoc.org.cn/pmo/class/PMO_00085363 PMAPP-PMO LOOM
http://purl.bioontology.org/ontology/OMIM/MTHU015031 OMIM LOOM
http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C3308 NCIT LOOM
http://purl.jp/bio/4/id/200906064578708779 IOBC LOOM
http://purl.bioontology.org/ontology/MESH/D010235 MESH LOOM
http://purl.bioontology.org/ontology/PDQ/CDR0000639696 PDQ LOOM
http://purl.obolibrary.org/obo/OMIT_0011232 OMIT LOOM
http://phenomebrowser.net/ontologies/mesh/mesh.owl#D010235 RH-MESH LOOM
http://sbmi.uth.tmc.edu/ontology/ochv#9261 OCHV LOOM
http://purl.bioontology.org/ontology/SNOMEDCT/302833002 SNOMEDCT LOOM
http://id.nlm.nih.gov/mesh/D010235 MDM LOOM
http://purl.obolibrary.org/obo/NCIT_C3308 BERO LOOM
http://purl.bioontology.org/ontology/SNOMEDCT/803009 SNOMEDCT LOOM
http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#Paraganglionic_Neoplasm CSEO LOOM
http://purl.obolibrary.org/obo/HP_0002668 HP LOOM
http://purl.obolibrary.org/obo/HP_0002668 UPHENO LOOM
http://sbmi.uth.tmc.edu/ontology/ochv#C0030421 OCHV LOOM
http://phenomebrowser.net/ontologies/mesh/mesh.owl#C04.557.580.625.650.700 RH-MESH LOOM