Medical Subject Headings

Last uploaded: January 31, 2024
Preferred Name

Kasabach-Merritt Syndrome

Synonyms

Syndrome, Thrombocytopenia-Hemangioma

Definitions

Rapidly growing vascular lesion along the midline axis of the neck, upper trunk, and extremities that is characterized by CONSUMPTION COAGULOPATHY; THROMBOCYTOPENIA; and HEMOLYTIC ANEMIA. It is often associated with infantile Kaposiform HEMANGIOENDOTHELIOMA and other vascular tumors such as tufted ANGIOMA.

ID

http://purl.bioontology.org/ontology/MESH/D059885

altLabel

Syndrome, Thrombocytopenia-Hemangioma

Kasabach Merritt Syndrome

Hemangioma Thrombocytopenia Syndrome

Kasabach Merritt Phenomenon

Thrombocytopenia-Hemangioma Syndromes

Thrombocytopenia-Hemangioma Syndrome

Syndrome, Kasabach-Merritt

Hemangioma Thrombocytopenia Syndromes

Syndromes, Thrombocytopenia-Hemangioma

Phenomenon, Kasabach-Merritt

Kasabach-Merritt Phenomenon

Thrombocytopenia Hemangioma Syndrome

Syndromes, Hemangioma Thrombocytopenia

Syndrome, Hemangioma Thrombocytopenia

Hemangioma-Thrombocytopenia Syndrome

AQL

BL BS CF CH CI CL CN CO DG DH DI DT EC EH EM EN EP ET GE HI IM ME MI MO NU PA PC PP PS PX RH RT SC SU TH UL UR VE VI

cui

C0221025

DC

1

definition

Rapidly growing vascular lesion along the midline axis of the neck, upper trunk, and extremities that is characterized by CONSUMPTION COAGULOPATHY; THROMBOCYTOPENIA; and HEMOLYTIC ANEMIA. It is often associated with infantile Kaposiform HEMANGIOENDOTHELIOMA and other vascular tumors such as tufted ANGIOMA.

DX

20120101

HN

2012

Inverse of AQ

http://purl.bioontology.org/ontology/MESH/Q000097

http://purl.bioontology.org/ontology/MESH/Q000098

http://purl.bioontology.org/ontology/MESH/Q000178

http://purl.bioontology.org/ontology/MESH/Q000175

http://purl.bioontology.org/ontology/MESH/Q000628

http://purl.bioontology.org/ontology/MESH/Q000648

http://purl.bioontology.org/ontology/MESH/Q000276

http://purl.bioontology.org/ontology/MESH/Q000134

http://purl.bioontology.org/ontology/MESH/Q000139

http://purl.bioontology.org/ontology/MESH/Q000266

http://purl.bioontology.org/ontology/MESH/Q000378

http://purl.bioontology.org/ontology/MESH/Q000517

http://purl.bioontology.org/ontology/MESH/Q000662

http://purl.bioontology.org/ontology/MESH/Q000469

http://purl.bioontology.org/ontology/MESH/Q000151

http://purl.bioontology.org/ontology/MESH/Q000150

http://purl.bioontology.org/ontology/MESH/Q000821

http://purl.bioontology.org/ontology/MESH/Q000191

http://purl.bioontology.org/ontology/MESH/Q000196

http://purl.bioontology.org/ontology/MESH/Q000473

http://purl.bioontology.org/ontology/MESH/Q000145

http://purl.bioontology.org/ontology/MESH/Q000737

http://purl.bioontology.org/ontology/MESH/Q000382

http://purl.bioontology.org/ontology/MESH/Q000451

http://purl.bioontology.org/ontology/MESH/Q000453

http://purl.bioontology.org/ontology/MESH/Q000534

http://purl.bioontology.org/ontology/MESH/Q000532

http://purl.bioontology.org/ontology/MESH/Q000503

http://purl.bioontology.org/ontology/MESH/Q000188

http://purl.bioontology.org/ontology/MESH/Q000235

http://purl.bioontology.org/ontology/MESH/Q000201

http://purl.bioontology.org/ontology/MESH/Q000209

http://purl.bioontology.org/ontology/MESH/Q000208

http://purl.bioontology.org/ontology/MESH/Q000601

http://purl.bioontology.org/ontology/MESH/Q000000981

http://purl.bioontology.org/ontology/MESH/Q000556

http://purl.bioontology.org/ontology/MESH/Q000652

http://purl.bioontology.org/ontology/MESH/Q000523

http://purl.bioontology.org/ontology/MESH/Q000401

Machine permutation

2012

Mapped from

http://purl.bioontology.org/ontology/MESH/C537007

MDA

20110624

MMR

20230226

MN

C15.378.243.937.645

C04.557.645.375.617

C15.378.140.855.645

notation

D059885

prefLabel

Kasabach-Merritt Syndrome

TERMUI

T780986

T780985

T800730

T780984

T780983

TH

OMIM (2013)

NLM (2012)

NLM (2013)

ORD (2010)

tui

T047

subClassOf

http://purl.bioontology.org/ontology/MESH/D013921

http://purl.bioontology.org/ontology/MESH/D006391

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http://purl.bioontology.org/ontology/MDRGER/10051768 MDRGER CUI
http://purl.bioontology.org/ontology/MDRGER/10051769 MDRGER CUI
http://purl.bioontology.org/ontology/MDRGER/10058423 MDRGER CUI
http://purl.bioontology.org/ontology/MDRFRE/10058423 MDRFRE CUI
http://purl.bioontology.org/ontology/MDRFRE/10051768 MDRFRE CUI
http://purl.bioontology.org/ontology/SNMI/DC-61120 SNMI CUI
http://purl.bioontology.org/ontology/OMIM/MTHU041322 OMIM CUI
http://purl.bioontology.org/ontology/SCTSPA/86635005 SCTSPA CUI
http://purl.bioontology.org/ontology/NDFRT/N0000183384 NDFRT CUI
http://purl.bioontology.org/ontology/OMIM/141000 OMIM CUI
http://purl.bioontology.org/ontology/CSP/2007-1757 CRISP CUI
http://purl.bioontology.org/ontology/MDRFRE/10051769 MDRFRE CUI
http://purl.bioontology.org/ontology/SNOMEDCT/86635005 SNOMEDCT CUI
http://purl.bioontology.org/ontology/MEDDRA/10051768 MEDDRA CUI
http://purl.bioontology.org/ontology/MEDDRA/10051769 MEDDRA CUI
http://purl.bioontology.org/ontology/MEDDRA/10058423 MEDDRA CUI
http://purl.bioontology.org/ontology/RCD/X78UT RCD CUI
http://purl.bioontology.org/ontology/MSHFRE/D059885 MSHFRE CUI
http://purl.bioontology.org/ontology/CSP/0446-5652 CRISP CUI
http://nanbyodata.jp/ontology/NANDO_2201035 NANDO LOOM
http://nanbyodata.jp/ontology/NANDO_2100297 NANDO LOOM
http://purl.obolibrary.org/obo/MONDO_0007708 MONDO LOOM
http://phenomebrowser.net/ontologies/mesh/mesh.owl#C04.557.645.375.617 RH-MESH LOOM
http://sbmi.uth.tmc.edu/ontology/ochv#C0221025 OCHV LOOM
http://purl.bioontology.org/ontology/SNMI/DC-61120 SNMI LOOM
http://purl.bioontology.org/ontology/OMIM/MTHU041322 OMIM LOOM
http://www.phoc.org.cn/pmo/class/PMO_00038051 PMAPP-PMO LOOM
http://purl.bioontology.org/ontology/SNOMEDCT/86635005 SNOMEDCT LOOM
http://purl.bioontology.org/ontology/MEDDRA/10051768 MEDDRA LOOM
http://www.limics.org/hrdo/rdfns#pat_id_3399 HRDO LOOM
http://purl.obolibrary.org/obo/OMIT_0027686 OMIT LOOM
http://phenomebrowser.net/ontologies/mesh/mesh.owl#C15.378.140.855.645 RH-MESH LOOM
http://purl.jp/bio/4/id/200906072756683265 IOBC LOOM
http://phenomebrowser.net/ontologies/mesh/mesh.owl#D059885 RH-MESH LOOM
http://www.limics.fr/ontologies/ontolurgences#SyndromeDeKasabachMerritt ONTOLURGENCES LOOM
http://id.nlm.nih.gov/mesh/D059885 MDM LOOM
http://www.owl-ontologies.com/unnamed.owl#RID18908 DERMLEX LOOM
http://purl.obolibrary.org/obo/MONDO_0007708 DOVES LOOM
http://www.gamuts.net/entity#Kasabach_Merritt_syndrome GAMUTS LOOM