Medical Subject Headings

Last uploaded: January 31, 2024
Preferred Name

Paget Disease, Extramammary

Synonyms

Extra Mammary Paget Disease

Pagets Disease, Extramammary

Extramammary Paget Disease

Paget Disease, Extra Mammary

Paget's Disease, Extramammary

Extra Mammary Paget's Disease

Extra-Mammary Paget's Disease

Extra-Mammary Pagets Disease

Paget Disease, Extra-Mammary

Extramammary, Paget Disease

Extramammary Pagets Disease

Paget's Disease, Extra-Mammary

Extramammary Paget's Disease

Paget's Disease, Extra Mammary

Pagets Disease, Extra-Mammary

Extra-Mammary Paget Disease

Paget Disease Extramammary

Definitions

A rare cutaneous neoplasm that occurs in the elderly. It develops more frequently in women and predominantly involves apocrine gland-bearing areas, especially the vulva, scrotum, and perianal areas. The lesions develop as erythematous scaly patches that progress to crusted, pruritic, erythematous plaques. The clinical differential diagnosis includes squamous cell carcinoma in situ and superficial fungal infection. It is generally thought to be an adenocarcinoma of the epidermis, from which it extends into the contiguous epithelium of hair follicles and eccrine sweat ducts. (DeVita Jr et al., Cancer: Principles & Practice of Oncology, 3d ed, p1478)

ID

http://purl.bioontology.org/ontology/MESH/D010145

altLabel

Extra Mammary Paget Disease

Pagets Disease, Extramammary

Extramammary Paget Disease

Paget Disease, Extra Mammary

Paget's Disease, Extramammary

Extra Mammary Paget's Disease

Extra-Mammary Paget's Disease

Extra-Mammary Pagets Disease

Paget Disease, Extra-Mammary

Extramammary, Paget Disease

Extramammary Pagets Disease

Paget's Disease, Extra-Mammary

Extramammary Paget's Disease

Paget's Disease, Extra Mammary

Pagets Disease, Extra-Mammary

Extra-Mammary Paget Disease

Paget Disease Extramammary

AN

neoplastic; coordinate with precoordinated organ/neoplasm term

AQL

BL BS CF CH CI CL CN CO DG DH DI DT EC EH EM EN EP ET GE HI IM ME MI MO NU PA PC PP PS PX RH RT SC SU TH UL UR VE VI

cui

C0030186

DC

1

definition

A rare cutaneous neoplasm that occurs in the elderly. It develops more frequently in women and predominantly involves apocrine gland-bearing areas, especially the vulva, scrotum, and perianal areas. The lesions develop as erythematous scaly patches that progress to crusted, pruritic, erythematous plaques. The clinical differential diagnosis includes squamous cell carcinoma in situ and superficial fungal infection. It is generally thought to be an adenocarcinoma of the epidermis, from which it extends into the contiguous epithelium of hair follicles and eccrine sweat ducts. (DeVita Jr et al., Cancer: Principles & Practice of Oncology, 3d ed, p1478)

DX

20100101

HN

2010(1963)

Inverse of AQ

http://purl.bioontology.org/ontology/MESH/Q000097

http://purl.bioontology.org/ontology/MESH/Q000098

http://purl.bioontology.org/ontology/MESH/Q000178

http://purl.bioontology.org/ontology/MESH/Q000175

http://purl.bioontology.org/ontology/MESH/Q000628

http://purl.bioontology.org/ontology/MESH/Q000648

http://purl.bioontology.org/ontology/MESH/Q000276

http://purl.bioontology.org/ontology/MESH/Q000134

http://purl.bioontology.org/ontology/MESH/Q000139

http://purl.bioontology.org/ontology/MESH/Q000266

http://purl.bioontology.org/ontology/MESH/Q000378

http://purl.bioontology.org/ontology/MESH/Q000517

http://purl.bioontology.org/ontology/MESH/Q000662

http://purl.bioontology.org/ontology/MESH/Q000469

http://purl.bioontology.org/ontology/MESH/Q000151

http://purl.bioontology.org/ontology/MESH/Q000150

http://purl.bioontology.org/ontology/MESH/Q000821

http://purl.bioontology.org/ontology/MESH/Q000191

http://purl.bioontology.org/ontology/MESH/Q000196

http://purl.bioontology.org/ontology/MESH/Q000473

http://purl.bioontology.org/ontology/MESH/Q000145

http://purl.bioontology.org/ontology/MESH/Q000737

http://purl.bioontology.org/ontology/MESH/Q000382

http://purl.bioontology.org/ontology/MESH/Q000451

http://purl.bioontology.org/ontology/MESH/Q000453

http://purl.bioontology.org/ontology/MESH/Q000534

http://purl.bioontology.org/ontology/MESH/Q000532

http://purl.bioontology.org/ontology/MESH/Q000503

http://purl.bioontology.org/ontology/MESH/Q000188

http://purl.bioontology.org/ontology/MESH/Q000235

http://purl.bioontology.org/ontology/MESH/Q000201

http://purl.bioontology.org/ontology/MESH/Q000209

http://purl.bioontology.org/ontology/MESH/Q000208

http://purl.bioontology.org/ontology/MESH/Q000601

http://purl.bioontology.org/ontology/MESH/Q000000981

http://purl.bioontology.org/ontology/MESH/Q000556

http://purl.bioontology.org/ontology/MESH/Q000652

http://purl.bioontology.org/ontology/MESH/Q000523

http://purl.bioontology.org/ontology/MESH/Q000401

Machine permutation

2010; see PAGET'S DISEASE, EXTRAMAMMARY 1994-2009, see PAGET'S DISEASE, EXTRA-MAMMARY 1963-1993

MDA

19990101

MMR

20120703

MN

C04.557.470.615.660

C04.557.470.200.025.660

notation

D010145

prefLabel

Paget Disease, Extramammary

TERMUI

T030047

T030041

T030044

T751079

T030046

T030040

T030045

T030043

T030042

TH

OMIM (2013)

NLM (1966)

NLM (1994)

NLM (1992)

UNK (19XX)

NLM (2010)

ORD (2010)

tui

T191

subClassOf

http://purl.bioontology.org/ontology/MESH/D018299

http://purl.bioontology.org/ontology/MESH/D000230

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Delete Mapping To Ontology Source
http://purl.bioontology.org/ontology/MDRGER/10033366 MDRGER CUI
http://purl.bioontology.org/ontology/MDRGER/10068223 MDRGER CUI
http://purl.bioontology.org/ontology/MEDDRA/10068223 MEDDRA CUI
http://purl.bioontology.org/ontology/MSHFRE/D010145 MSHFRE CUI
http://purl.bioontology.org/ontology/SCTSPA/232336001 SCTSPA CUI
http://purl.bioontology.org/ontology/MDRFRE/10033366 MDRFRE CUI
http://purl.bioontology.org/ontology/RCD/X00kl RCD CUI
http://purl.bioontology.org/ontology/RCD/Xa98z RCD CUI
http://purl.bioontology.org/ontology/SNOMEDCT/232336001 SNOMEDCT CUI
http://purl.bioontology.org/ontology/MEDDRA/10033366 MEDDRA CUI
http://purl.bioontology.org/ontology/OMIM/167300 OMIM CUI
http://purl.bioontology.org/ontology/SNOMEDCT/71447003 SNOMEDCT CUI
http://purl.bioontology.org/ontology/MDRFRE/10068223 MDRFRE CUI
http://purl.bioontology.org/ontology/NDFRT/N0000002277 NDFRT CUI
http://purl.bioontology.org/ontology/SNMI/M-85423 SNMI CUI
http://purl.bioontology.org/ontology/SCTSPA/71447003 SCTSPA CUI
http://phenomebrowser.net/ontologies/mesh/mesh.owl#D010145 RH-MESH LOOM
http://purl.obolibrary.org/obo/OMIT_0011148 OMIT LOOM
http://id.nlm.nih.gov/mesh/D010145 MDM LOOM
http://phenomebrowser.net/ontologies/mesh/mesh.owl#C04.557.470.615.660 RH-MESH LOOM
http://phenomebrowser.net/ontologies/mesh/mesh.owl#C04.557.470.200.025.660 RH-MESH LOOM
http://www.phoc.org.cn/pmo/class/PMO_00037986 PMAPP-PMO LOOM
http://purl.bioontology.org/ontology/OMIM/167300 OMIM LOOM