Preferred Name |
Glomerulosclerosis, Focal Segmental |
|
Synonyms |
Focal Sclerosing Glomerulonephritides |
|
Definitions |
A clinicopathological syndrome or diagnostic term for a type of glomerular injury that has multiple causes, primary or secondary. Clinical features include PROTEINURIA, reduced GLOMERULAR FILTRATION RATE, and EDEMA. Kidney biopsy initially indicates focal segmental glomerular consolidation (hyalinosis) or scarring which can progress to globally sclerotic glomeruli leading to eventual KIDNEY FAILURE. |
|
ID |
http://purl.bioontology.org/ontology/MESH/D005923 |
|
altLabel |
Focal Sclerosing Glomerulonephritides Segmental Hyalinosis Glomerulonephritides, Focal Sclerosing Glomerulonephritis, Focal Sclerosing Glomerular Hyalinosis, Segmental Focal Sclerosing Glomerulonephritis Sclerosing Glomerulonephritis, Focal Segmental Glomerular Hyalinosis Focal Segmental Glomerulosclerosis Hyalinosis, Segmental Glomerular Sclerosing Glomerulonephritides, Focal Segmental Glomerulosclerosis, Focal Focal Glomerulosclerosis Glomerulosclerosis, Focal Hyalinosis, Segmental |
|
AQL |
BL CF CI CL CN CO DG DH DI DT EC EH EM EN EP ET GE HI IM ME MI MO NU PA PC PP PS PX RH RT SU TH UR VE VI |
|
cui |
C0086432 C0017668 |
|
DC |
1 |
|
definition |
A clinicopathological syndrome or diagnostic term for a type of glomerular injury that has multiple causes, primary or secondary. Clinical features include PROTEINURIA, reduced GLOMERULAR FILTRATION RATE, and EDEMA. Kidney biopsy initially indicates focal segmental glomerular consolidation (hyalinosis) or scarring which can progress to globally sclerotic glomeruli leading to eventual KIDNEY FAILURE. Segmental glomerular degeneration with a glassy appearance (hyalinosis) caused by the accumulation of plasma proteins in the glomeruli. |
|
DX |
19910101 |
|
HN |
2007 (1977) |
|
Inverse of AQ |
http://purl.bioontology.org/ontology/MESH/Q000097 http://purl.bioontology.org/ontology/MESH/Q000178 http://purl.bioontology.org/ontology/MESH/Q000175 http://purl.bioontology.org/ontology/MESH/Q000628 http://purl.bioontology.org/ontology/MESH/Q000276 http://purl.bioontology.org/ontology/MESH/Q000134 http://purl.bioontology.org/ontology/MESH/Q000139 http://purl.bioontology.org/ontology/MESH/Q000266 http://purl.bioontology.org/ontology/MESH/Q000378 http://purl.bioontology.org/ontology/MESH/Q000517 http://purl.bioontology.org/ontology/MESH/Q000662 http://purl.bioontology.org/ontology/MESH/Q000469 http://purl.bioontology.org/ontology/MESH/Q000151 http://purl.bioontology.org/ontology/MESH/Q000150 http://purl.bioontology.org/ontology/MESH/Q000821 http://purl.bioontology.org/ontology/MESH/Q000191 http://purl.bioontology.org/ontology/MESH/Q000196 http://purl.bioontology.org/ontology/MESH/Q000473 http://purl.bioontology.org/ontology/MESH/Q000145 http://purl.bioontology.org/ontology/MESH/Q000382 http://purl.bioontology.org/ontology/MESH/Q000451 http://purl.bioontology.org/ontology/MESH/Q000453 http://purl.bioontology.org/ontology/MESH/Q000534 http://purl.bioontology.org/ontology/MESH/Q000532 http://purl.bioontology.org/ontology/MESH/Q000503 http://purl.bioontology.org/ontology/MESH/Q000188 http://purl.bioontology.org/ontology/MESH/Q000235 http://purl.bioontology.org/ontology/MESH/Q000201 http://purl.bioontology.org/ontology/MESH/Q000209 http://purl.bioontology.org/ontology/MESH/Q000208 http://purl.bioontology.org/ontology/MESH/Q000601 http://purl.bioontology.org/ontology/MESH/Q000000981 http://purl.bioontology.org/ontology/MESH/Q000652 |
|
Machine permutation |
2007; see GLOMERULOSCLEROSIS, FOCAL 1991-2006, GLOMERULONEPHRITIS 1977-1990 |
|
Mapped from |
http://purl.bioontology.org/ontology/MESH/C538457 |
|
MDA |
19760519 |
|
MMR |
20210630 |
|
MN |
C12.200.777.419.570.363.660 C12.050.351.968.419.570.363.640 C12.950.419.570.363.640 |
|
notation |
D005923 |
|
prefLabel |
Glomerulosclerosis, Focal Segmental |
|
TERMUI |
T017925 T017926 T656941 T656939 T656940 T656938 T017927 |
|
TH |
OMIM (2013) NLM (1977) UNK (19XX) NLM (2007) ORD (2010) |
|
tui |
T047 |
|
subClassOf |