loading...| Preferred Name | Kaposiform Hemangioendothelioma | |
| Synonyms |
Kaposiform hemangio-endothelioma Congenital cutaneous multifocal kaposiform hemangioendothelioma |
|
| ID |
http://purl.bioontology.org/ontology/MESH/C537007 |
|
| altLabel |
Kaposiform hemangio-endothelioma Congenital cutaneous multifocal kaposiform hemangioendothelioma |
|
| cui |
C1367420 |
|
| HM |
D012514 D059885 D006390 |
|
| Inverse of RB |
0 |
|
| Mapped to |
http://purl.bioontology.org/ontology/MESH/D012514 |
|
| MDA |
20100825 |
|
| MeSH Frequency |
199 |
|
| MMR |
20160719 |
|
| notation |
C537007 |
|
| prefLabel |
Kaposiform Hemangioendothelioma |
|
| SC |
3 |
|
| Scope Statement |
A rare, locally aggressive vascular neoplasm that primarily occurs in childhood. It originates on the skin and is characterized by one or multiple masse; it is often comorbid with Kasabach-Merritt syndrome and lymphangiomatosis. The viscera is usually not affected, but invasion of bone, retroperitoneum, and MEDIASTINUM has occured in some cases. No metastases have been reported. |
|
| TERMUI |
T741157 T741159 T741161 |
|
| TH |
ORD (2010) |
|
| tui |
T191 |