Preferred Name |
Dermatofibrosarcoma protuberans |
|
Synonyms |
DFSP |
|
ID |
http://www.limics.org/hrdo/rdfns#pat_id_9285 |
|
ageOfDeath |
Adult Adulto Adult Erwachsene Adulti Adultos Adulte |
|
ageOfOnset |
Variable Variabile Variabel Variable Variable Variável Variable |
|
altLabel |
DFSP DFSP DFSP |
|
id_MedDRA |
10057070 |
|
id_Medline |
neant |
|
id_MeSH |
C538219 |
|
id_MIM |
607907 |
|
id_Orpha |
31112 |
|
id_SNOMEDCT |
128742004 238863004 276799004 |
|
id_UMLS |
C0392784 |
|
inheritance |
Esporádico Sporadic Sporadisch Sporadique Sporadica Sporadic Esporádica |
|
patType |
disease |
|
prefixIRI |
hrdo:pat_id_9285 |
|
prefLabel |
Dermatofibrosarcoma protuberante Dermatofibrossarcoma protuberante Dermatofibrosarcoma di Darier-Ferrand Dermatofibrosarcome de Darier-Ferrand Dermatofibrosarcoma protuberans Dermatofibrosarcoma protuberans |
|
prevalence |
1-5 / 10 000 1-5 / 10 000 1-5 / 10 000 1-5 / 10 000 1-5 / 10 000 1-5 / 10 000 1-5 / 10 000 |
|
subClassOf |
Create mapping