Preferred Name

Heritable pulmonary arterial hypertension

Synonyms

Pulmonale arterielle Hypertonie, familiäre

FPAH

Ipertensione arteriosa polmonare familiare

Familial pulmonary arterial hypertension

ID

http://www.limics.org/hrdo/rdfns#pat_id_20328

ageOfDeath

Cualquier edad

Alle Alter

Qualquer idade

Tout âge

Any age

Qualsiasi età

Any age

ageOfOnset

Variable

Variabile

Variabel

Variable

Variable

Variável

Variable

altLabel

Pulmonale arterielle Hypertonie, familiäre

FPAH

Ipertensione arteriosa polmonare familiare

FPAH

Familial pulmonary arterial hypertension

Ipertensione arteriosa polmonare ereditaria

Hipertensión arterial pulmonar familiar

Hypertension artérielle pulmonaire familiale

HAPH

HTAPf

Hereditary pulmonary arterial hypertension

FPAH

FPAH

id_Medline

neant

id_OMS

I27.0

id_Orpha

275777

inheritance

Autosomal dominant

Autosomique dominant

Autosomal dominant

Autosomica dominante

Autosómico dominate

Autosomal-dominant

Autossómica dominante

patType

etiological subtype

prefixIRI

hrdo:pat_id_20328

prefLabel

Heritable pulmonary arterial hypertension

Ipertensione arteriosa polmonare ereditabile

Pulmonale arterielle Hypertonie, hereditäre

Hypertension artérielle pulmonaire héréditaire

Hipertensión arterial pulmonar hereditaria

Heritable pulmonary arterial hypertension

prevalence

Inconnu

Unknown

Unknown

Desconocido

Unbekannt

Desconhecido

Sconosciuto

subClassOf

http://www.limics.org/hrdo/rdfns#typ_id_5

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