Preferred Name |
Heritable pulmonary arterial hypertension |
|
Synonyms |
Pulmonale arterielle Hypertonie, familiäre FPAH Ipertensione arteriosa polmonare familiare Familial pulmonary arterial hypertension |
|
ID |
http://www.limics.org/hrdo/rdfns#pat_id_20328 |
|
ageOfDeath |
Cualquier edad Alle Alter Qualquer idade Tout âge Any age Qualsiasi età Any age |
|
ageOfOnset |
Variable Variabile Variabel Variable Variable Variável Variable |
|
altLabel |
Pulmonale arterielle Hypertonie, familiäre FPAH Ipertensione arteriosa polmonare familiare FPAH Familial pulmonary arterial hypertension Ipertensione arteriosa polmonare ereditaria Hipertensión arterial pulmonar familiar Hypertension artérielle pulmonaire familiale HAPH HTAPf Hereditary pulmonary arterial hypertension FPAH FPAH |
|
id_Medline |
neant |
|
id_OMS |
I27.0 |
|
id_Orpha |
275777 |
|
inheritance |
Autosomal dominant Autosomique dominant Autosomal dominant Autosomica dominante Autosómico dominate Autosomal-dominant Autossómica dominante |
|
patType |
etiological subtype |
|
prefixIRI |
hrdo:pat_id_20328 |
|
prefLabel |
Heritable pulmonary arterial hypertension Ipertensione arteriosa polmonare ereditabile Pulmonale arterielle Hypertonie, hereditäre Hypertension artérielle pulmonaire héréditaire Hipertensión arterial pulmonar hereditaria Heritable pulmonary arterial hypertension |
|
prevalence |
Inconnu Unknown Unknown Desconocido Unbekannt Desconhecido Sconosciuto |
|
subClassOf |