Preferred Name |
Pulmonary arterial hypertension |
|
Synonyms |
PAH HAP |
|
ID |
http://www.limics.org/hrdo/rdfns#pat_id_18210 |
|
ageOfOnset |
Variable Variabile Variabel Variable Variable Variável Variable |
|
altLabel |
PAH PAH HAP PAH |
|
id_MedDRA |
10064911 |
|
id_MeSH |
C536282 |
|
id_Orpha |
182090 |
|
id_SNOMEDCT |
26174007 |
|
id_UMLS |
C0152171 |
|
inheritance |
Autosomal dominant Autosomique dominant Esporádico Autosomal dominant Autosomica dominante Autosómico dominate Sporadic Sporadisch Sporadique Autosomal-dominant Sporadica Sporadic Autossómica dominante Esporádica |
|
patType |
group of phenomes |
|
prefixIRI |
hrdo:pat_id_18210 |
|
prefLabel |
Hypertension artérielle pulmonaire Pulmonary arterial hypertension Ipertensione arteriosa polmonare Hipertensão arterial pulmonar Hypertension, arterielle pulmonale Hipertensión arterial pulmonar |
|
prevalence |
1-9 / 100 000 1-9 / 100 000 1-9 / 100 000 1-9 / 100 000 1-9 / 100 000 1-9 / 100 000 1-9 / 100 000 |
|
subClassOf |
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