Preferred Name |
pancreatic endocrine carcinoma |
|
Synonyms |
neuroendocrine carcinoma of pancreas high grade pancreatic neuroendocrine carcinoma malignant neoplasm of islets of Langerhans pancreatic NEC poorly-differentiated NEN of pancreas islet cell carcinoma (morphologic abnormality) Pancreatic Neuroendocrine cancer carcinoma, islet cell, malignant pancreatic NEC G3 malignant pancreatic endocrine tumor poorly-differentiated pancreatic NEN poorly-differentiated pancreatic neuroendocrine neoplasm islet cell carcinoma malignant islet cell tumor pancreatic endocrine cancer islet cell cancer poorly differentiated pancreatic endocrine carcinoma pancreatic neuroendocrine carcinoma pancreatic endocrine carcinoma malignant pancreatic endocrine tumour carcinoma of endocrine pancreas malignant islet cell tumour poorly-differentiated neuroendocrine neoplasm of pancreas high-grade pancreatic neuroendocrine carcinoma endocrine pancreas carcinoma |
|
Definitions |
An aggressive, high-grade and poorly differentiated carcinoma with neuroendocrine differentiation that arises from the pancreas. The mitotic count is more than 20 per 10 HPF. According to the size of the malignant cells, the prominence of the nucleoli, and the amount of cytoplasm, it is classified either as small or large cell neuroendocrine carcinoma. |
|
ID |
http://purl.obolibrary.org/obo/MONDO_0005893 |
|
conformsTo |
http://purl.obolibrary.org/obo/mondo/patterns/carcinoma.yaml |
|
exactMatch |
http://purl.obolibrary.org/obo/NCIT_C3770 http://purl.bioontology.org/ontology/ICD10CM/C25.4 http://linkedlifedata.com/resource/umls/id/C1328479 http://www.orpha.net/ORDO/Orphanet_506098 http://identifiers.org/snomedct/254612002 |
|
hasDbXref |
Orphanet:506098 ICDO:8150/3 UMLS:C1328479 SCTID:254612002 EFO:0007416 MESH:D018273 ICD10CM:C25.4 DOID:1798 GARD:22056 ICD9:157.4 NCIT:C3770 |
|
hasExactSynonym |
high grade pancreatic neuroendocrine carcinoma malignant neoplasm of islets of Langerhans pancreatic NEC poorly-differentiated NEN of pancreas islet cell carcinoma (morphologic abnormality) Pancreatic Neuroendocrine cancer carcinoma, islet cell, malignant pancreatic NEC G3 malignant pancreatic endocrine tumor poorly-differentiated pancreatic NEN poorly-differentiated pancreatic neuroendocrine neoplasm islet cell carcinoma malignant islet cell tumor pancreatic endocrine cancer islet cell cancer poorly differentiated pancreatic endocrine carcinoma pancreatic neuroendocrine carcinoma pancreatic endocrine carcinoma malignant pancreatic endocrine tumour carcinoma of endocrine pancreas malignant islet cell tumour poorly-differentiated neuroendocrine neoplasm of pancreas high-grade pancreatic neuroendocrine carcinoma endocrine pancreas carcinoma |
|
hasRelatedSynonym |
neuroendocrine carcinoma of pancreas |
|
IAO_0000115 |
An aggressive, high-grade and poorly differentiated carcinoma with neuroendocrine differentiation that arises from the pancreas. The mitotic count is more than 20 per 10 HPF. According to the size of the malignant cells, the prominence of the nucleoli, and the amount of cytoplasm, it is classified either as small or large cell neuroendocrine carcinoma. |
|
id |
MONDO:0005893 |
|
inSubset |
http://purl.obolibrary.org/obo/mondo#ordo_disease http://purl.obolibrary.org/obo/mondo#rare http://purl.obolibrary.org/obo/mondo#nord_rare |
|
label |
pancreatic endocrine carcinoma |
|
notation |
MONDO:0005893 |
|
prefLabel |
pancreatic endocrine carcinoma |
|
subClassOf |
http://purl.obolibrary.org/obo/MONDO_0005815 http://purl.obolibrary.org/obo/MONDO_0004993 http://purl.obolibrary.org/obo/MONDO_0002120 |