Global Code Book Ontology

Last uploaded: May 2, 2024
Preferred Name

pancreatic endocrine carcinoma

Synonyms

neuroendocrine carcinoma of pancreas

high grade pancreatic neuroendocrine carcinoma

malignant neoplasm of islets of Langerhans

pancreatic NEC

poorly-differentiated NEN of pancreas

islet cell carcinoma (morphologic abnormality)

Pancreatic Neuroendocrine cancer

carcinoma, islet cell, malignant

pancreatic NEC G3

malignant pancreatic endocrine tumor

poorly-differentiated pancreatic NEN

poorly-differentiated pancreatic neuroendocrine neoplasm

islet cell carcinoma

malignant islet cell tumor

pancreatic endocrine cancer

islet cell cancer

poorly differentiated pancreatic endocrine carcinoma

pancreatic neuroendocrine carcinoma

pancreatic endocrine carcinoma

malignant pancreatic endocrine tumour

carcinoma of endocrine pancreas

malignant islet cell tumour

poorly-differentiated neuroendocrine neoplasm of pancreas

high-grade pancreatic neuroendocrine carcinoma

endocrine pancreas carcinoma

Definitions

An aggressive, high-grade and poorly differentiated carcinoma with neuroendocrine differentiation that arises from the pancreas. The mitotic count is more than 20 per 10 HPF. According to the size of the malignant cells, the prominence of the nucleoli, and the amount of cytoplasm, it is classified either as small or large cell neuroendocrine carcinoma.

ID

http://purl.obolibrary.org/obo/MONDO_0005893

conformsTo

http://purl.obolibrary.org/obo/mondo/patterns/carcinoma.yaml

exactMatch

http://purl.obolibrary.org/obo/NCIT_C3770

http://purl.bioontology.org/ontology/ICD10CM/C25.4

http://linkedlifedata.com/resource/umls/id/C1328479

http://www.orpha.net/ORDO/Orphanet_506098

http://identifiers.org/snomedct/254612002

http://identifiers.org/mesh/D018273

http://purl.obolibrary.org/obo/DOID_1798

hasDbXref

Orphanet:506098

ICDO:8150/3

UMLS:C1328479

SCTID:254612002

EFO:0007416

MESH:D018273

ICD10CM:C25.4

DOID:1798

GARD:22056

ICD9:157.4

NCIT:C3770

hasExactSynonym

high grade pancreatic neuroendocrine carcinoma

malignant neoplasm of islets of Langerhans

pancreatic NEC

poorly-differentiated NEN of pancreas

islet cell carcinoma (morphologic abnormality)

Pancreatic Neuroendocrine cancer

carcinoma, islet cell, malignant

pancreatic NEC G3

malignant pancreatic endocrine tumor

poorly-differentiated pancreatic NEN

poorly-differentiated pancreatic neuroendocrine neoplasm

islet cell carcinoma

malignant islet cell tumor

pancreatic endocrine cancer

islet cell cancer

poorly differentiated pancreatic endocrine carcinoma

pancreatic neuroendocrine carcinoma

pancreatic endocrine carcinoma

malignant pancreatic endocrine tumour

carcinoma of endocrine pancreas

malignant islet cell tumour

poorly-differentiated neuroendocrine neoplasm of pancreas

high-grade pancreatic neuroendocrine carcinoma

endocrine pancreas carcinoma

hasRelatedSynonym

neuroendocrine carcinoma of pancreas

IAO_0000115

An aggressive, high-grade and poorly differentiated carcinoma with neuroendocrine differentiation that arises from the pancreas. The mitotic count is more than 20 per 10 HPF. According to the size of the malignant cells, the prominence of the nucleoli, and the amount of cytoplasm, it is classified either as small or large cell neuroendocrine carcinoma.

id

MONDO:0005893

inSubset

http://purl.obolibrary.org/obo/mondo#ordo_disease

http://purl.obolibrary.org/obo/mondo#rare

http://purl.obolibrary.org/obo/mondo#nord_rare

http://purl.obolibrary.org/obo/mondo#orphanet_rare

http://purl.obolibrary.org/obo/mondo#gard_rare

label

pancreatic endocrine carcinoma

notation

MONDO:0005893

prefLabel

pancreatic endocrine carcinoma

subClassOf

http://purl.obolibrary.org/obo/MONDO_0005815

http://purl.obolibrary.org/obo/MONDO_0004993

http://purl.obolibrary.org/obo/MONDO_0002120

http://purl.obolibrary.org/obo/MONDO_0006181

http://purl.obolibrary.org/obo/MONDO_0009831

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