Preferred Name |
granulomatosis with polyangiitis |
|
Synonyms |
Wegener granulomatosis, formerly Necrotizing respiratory granulomatosis |
|
Definitions |
An autoimmune hypersensitivity disease that is characterized by necrotizing granulomatous inflammation of the upper and lower respiratory tract, glomerulonephritis, vasculitis, and the presence of antineutrophil cytoplasmatic autoantibodies (ANCAs) in patient sera, and is located_in lung, located_in kidney, located_in skin resulting from an autoimmune attack by antineutrophil cytoplasmic antibodies against small and medium-size blood vessels. |
|
ID |
http://purl.obolibrary.org/obo/DOID_12132 |
|
database_cross_reference |
MTHICD9_2006:446.4 UMLS_CUI:C3495801 ICD10CM:M31.30 ICD10CM:M31.3 ICD9CM:446.4 OMIM:608710 MESH:D014890 SNOMEDCT_US_2018_03_01:23782005 GARD:7880 NCI:C3444 |
|
fromArticle |
true |
|
has exact synonym |
Wegener granulomatosis, formerly Necrotizing respiratory granulomatosis |
|
has_obo_namespace |
disease_ontology |
|
id |
DOID:12132 |
|
imported from | ||
in subset | ||
label |
granulomatosis with polyangiitis |
|
notation |
DOID:12132 |
|
prefLabel |
granulomatosis with polyangiitis |
|
see also |
https://www.epilepsy.com/learn/professionals/challenging-cases/granulomatosis-polyangiitis |
|
文本定义 |
An autoimmune hypersensitivity disease that is characterized by necrotizing granulomatous inflammation of the upper and lower respiratory tract, glomerulonephritis, vasculitis, and the presence of antineutrophil cytoplasmatic autoantibodies (ANCAs) in patient sera, and is located_in lung, located_in kidney, located_in skin resulting from an autoimmune attack by antineutrophil cytoplasmic antibodies against small and medium-size blood vessels. |
|
subClassOf |
http://purl.obolibrary.org/obo/DOID_37 http://purl.obolibrary.org/obo/DOID_417 |