EpilepsyOntology

Last uploaded: November 8, 2021
Preferred Name

granulomatosis with polyangiitis

Synonyms

Wegener granulomatosis, formerly

Necrotizing respiratory granulomatosis

Definitions

An autoimmune hypersensitivity disease that is characterized by necrotizing granulomatous inflammation of the upper and lower respiratory tract, glomerulonephritis, vasculitis, and the presence of antineutrophil cytoplasmatic autoantibodies (ANCAs) in patient sera, and is located_in lung, located_in kidney, located_in skin resulting from an autoimmune attack by antineutrophil cytoplasmic antibodies against small and medium-size blood vessels.

ID

http://purl.obolibrary.org/obo/DOID_12132

database_cross_reference

MTHICD9_2006:446.4

UMLS_CUI:C3495801

ICD10CM:M31.30

ICD10CM:M31.3

ICD9CM:446.4

OMIM:608710

MESH:D014890

SNOMEDCT_US_2018_03_01:23782005

GARD:7880

NCI:C3444

fromArticle

true

has exact synonym

Wegener granulomatosis, formerly

Necrotizing respiratory granulomatosis

has_obo_namespace

disease_ontology

id

DOID:12132

imported from

http://purl.obolibrary.org/obo/doid.owl

in subset

http://purl.oboInOwllibrary.org/oboInOwl/doid#NCIthesaurus

label

granulomatosis with polyangiitis

notation

DOID:12132

prefLabel

granulomatosis with polyangiitis

see also

https://www.epilepsy.com/learn/professionals/challenging-cases/granulomatosis-polyangiitis

文本定义

An autoimmune hypersensitivity disease that is characterized by necrotizing granulomatous inflammation of the upper and lower respiratory tract, glomerulonephritis, vasculitis, and the presence of antineutrophil cytoplasmatic autoantibodies (ANCAs) in patient sera, and is located_in lung, located_in kidney, located_in skin resulting from an autoimmune attack by antineutrophil cytoplasmic antibodies against small and medium-size blood vessels.

subClassOf

http://purl.obolibrary.org/obo/DOID_37

http://purl.obolibrary.org/obo/DOID_417

http://purl.obolibrary.org/obo/DOID_557

http://purl.obolibrary.org/obo/DOID_850

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Delete Mapping To Ontology Source
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