Preferred Name |
undifferentiated pleomorphic sarcoma |
|
Synonyms |
undifferentiated pleomorphic sarcoma/malignant fibrous histiocytoma/high-grade spindle cell sarcoma malignant fibrohistiocytic tumors malignant fibrohistiocytic tumours Storiform-pleomorphic MFH Unclassified Pleomorphic sarcoma (formerly "malignant fibrous histiocytoma") fibroxanthosarcoma fibrous histiocytoma, malignant (morphologic abnormality) adult malignant fibrous histiocytoma malignant fibrous histiocytoma of the soft tissue and bone malignant fibrous cytoma unclassified pleomorphic sarcoma fibrous histiocytoma, malignant Unclassified Pleomorphic sarcoma (formerly "MFH") adult unclassified pleomorphic sarcoma malignant fibrous histiocytoma Storiform-pleomorphic fibrous histiocytoma malignant fibrous histiocytoma of soft tissue and bone Storiform-pleomorphic malignant fibrous histiocytoma adult undifferentiated pleomorphic sarcoma fibroxanthosarcoma (morphologic abnormality) histiocytoma, fibrous, malignant undifferentiated pleomorphic sarcoma malignant fibroxanthoma undifferentiated pleomorphic soft tissue sarcoma MFH UPS |
|
Definitions |
An undifferentiated soft tissue sarcoma characterized by the presence of a pleomorphic malignant cellular infiltrate. It is also known as malignant fibrous histiocytoma. |
|
ID |
http://www.ebi.ac.uk/efo/EFO_1001972 |
|
closeMatch |
http://linkedlifedata.com/resource/umls/id/C0279546 http://identifiers.org/snomedct/34360000 |
|
database_cross_reference |
MedDRA:10025552 ONCOTREE:MFH NCIT:C114541 ICD10:C49.9 SCTID:443439001 MESH:D051677 EFO:1001972 ICDO:8830/3 GARD:0006963 Orphanet:2023 DOID:1907 GARD:6963 HGNC:16982 ICD9:171.9 NCIT:C4247 MONDO:0002142 |
|
definition |
An undifferentiated soft tissue sarcoma characterized by the presence of a pleomorphic malignant cellular infiltrate. It is also known as malignant fibrous histiocytoma. |
|
exactMatch |
http://identifiers.org/snomedct/443439001 http://purl.obolibrary.org/obo/NCIT_C114541 http://purl.obolibrary.org/obo/Orphanet_2023 http://purl.obolibrary.org/obo/DOID_1907 |
|
has_alternative_id |
MONDO:0016069 |
|
has_exact_synonym |
Storiform-pleomorphic MFH Unclassified Pleomorphic sarcoma (formerly "malignant fibrous histiocytoma") fibroxanthosarcoma fibrous histiocytoma, malignant (morphologic abnormality) adult malignant fibrous histiocytoma malignant fibrous histiocytoma of the soft tissue and bone malignant fibrous cytoma unclassified pleomorphic sarcoma fibrous histiocytoma, malignant Unclassified Pleomorphic sarcoma (formerly "MFH") adult unclassified pleomorphic sarcoma malignant fibrous histiocytoma Storiform-pleomorphic fibrous histiocytoma malignant fibrous histiocytoma of soft tissue and bone Storiform-pleomorphic malignant fibrous histiocytoma adult undifferentiated pleomorphic sarcoma fibroxanthosarcoma (morphologic abnormality) histiocytoma, fibrous, malignant undifferentiated pleomorphic sarcoma malignant fibroxanthoma undifferentiated pleomorphic soft tissue sarcoma MFH UPS |
|
has_related_synonym |
undifferentiated pleomorphic sarcoma/malignant fibrous histiocytoma/high-grade spindle cell sarcoma malignant fibrohistiocytic tumors malignant fibrohistiocytic tumours |
|
id |
EFO:1001972 |
|
in_subset |
http://purl.obolibrary.org/obo/mondo/mondo-base#rare http://purl.obolibrary.org/obo/mondo#ordo_disease http://purl.obolibrary.org/obo/mondo/mondo-base#otar http://purl.obolibrary.org/obo/mondo/mondo-base#gard_rare http://purl.obolibrary.org/obo/mondo/mondo-base#orphanet_rare http://purl.obolibrary.org/obo/mondo/mondo-base#nord_rare http://purl.obolibrary.org/obo/mondo#gard_rare http://purl.obolibrary.org/obo/mondo/mondo-base#ordo_disease |
|
label |
undifferentiated pleomorphic sarcoma |
|
notation |
EFO:1001972 |
|
preferred label |
undifferentiated pleomorphic sarcoma |
|
prefLabel |
undifferentiated pleomorphic sarcoma |
|
see also |
https://rarediseases.info.nih.gov/diseases/6963/undifferentiated-pleomorphic-sarcoma |
|
subClassOf |
http://purl.obolibrary.org/obo/MONDO_0021054 |