loading...| Preferred Name | persistent fetal circulation syndrome | |
| Synonyms |
Persistent fetal circulation persistent fetal circulation syndrome Persistent fetal circulation (disorder) persistent pulmonary hypertension of the newborn persistent fetal circulation Persistent Fetal Circulation Syndrome Persistent pulmonary hypertension of the newborn (disorder) Persistent fetal circulation syndrome (disorder) congenital alveolar capillary dysplasia with misalignment of pulmonary veins persistent foetal circulation Fetal circulation PPHN |
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| Definitions |
A syndrome of persistent PULMONARY HYPERTENSION in the newborn infant (INFANT, NEWBORN) without demonstrable HEART DISEASES. This neonatal condition can be caused by severe pulmonary vasoconstriction (reactive type), hypertrophy of pulmonary arterial muscle (hypertrophic type), or abnormally developed pulmonary arterioles (hypoplastic type). The newborn patient exhibits CYANOSIS and ACIDOSIS due to the persistence of fetal circulatory pattern of right-to-left shunting of blood through a patent ductus arteriosus (DUCTUS ARTERIOSUS, PATENT) and at times a patent foramen ovale (FORAMEN OVALE, PATENT). A cardiopulmonary disorder characterized by systemic arterial hypoxemia secondary to pulmonary hypertension and extrapulmonary right to left shunting across the foramen ovale and ductus arteriosus. |
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| ID |
http://www.ebi.ac.uk/efo/EFO_1001103 |
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| database_cross_reference |
MESH:D010547 OMIM:617039 OMIM:617035 NCIT:C85006 ICD10:P29.3 SCTID:233815004 SCTID:206597007 MeSH:D010547 UMLS:C0031190 MEDGEN:45824 SCTID:35604006 SNOMEDCT:35604006 NCIt:C85006 MONDO:0022430 MedDRA:10054726 DOID:13042 |
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| definition |
A syndrome of persistent PULMONARY HYPERTENSION in the newborn infant (INFANT, NEWBORN) without demonstrable HEART DISEASES. This neonatal condition can be caused by severe pulmonary vasoconstriction (reactive type), hypertrophy of pulmonary arterial muscle (hypertrophic type), or abnormally developed pulmonary arterioles (hypoplastic type). The newborn patient exhibits CYANOSIS and ACIDOSIS due to the persistence of fetal circulatory pattern of right-to-left shunting of blood through a patent ductus arteriosus (DUCTUS ARTERIOSUS, PATENT) and at times a patent foramen ovale (FORAMEN OVALE, PATENT). A cardiopulmonary disorder characterized by systemic arterial hypoxemia secondary to pulmonary hypertension and extrapulmonary right to left shunting across the foramen ovale and ductus arteriosus. |
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| exactMatch |
http://purl.obolibrary.org/obo/NCIT_C85006 http://purl.obolibrary.org/obo/EFO_1001103 http://identifiers.org/medgen/45824 http://linkedlifedata.com/resource/umls/id/C0031190 |
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| has_exact_synonym |
Persistent fetal circulation persistent fetal circulation syndrome Persistent fetal circulation (disorder) persistent pulmonary hypertension of the newborn persistent fetal circulation Persistent Fetal Circulation Syndrome Persistent pulmonary hypertension of the newborn (disorder) Persistent fetal circulation syndrome (disorder) congenital alveolar capillary dysplasia with misalignment of pulmonary veins persistent foetal circulation Fetal circulation PPHN |
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| IAO_0000233 | ||
| id |
EFO:1001103 |
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| in_subset | ||
| label |
persistent fetal circulation syndrome |
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| notation |
EFO:1001103 |
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| preferred label |
persistent fetal circulation syndrome |
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| prefLabel |
persistent fetal circulation syndrome |
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| relatedMatch | ||
| term editor |
Dani Welter |
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| subClassOf |
http://www.ebi.ac.uk/efo/EFO_0010238 |