loading...| Preferred Name |
pancreatic neuroendocrine tumor |
|
| Synonyms |
neuroendocrine tumor of pancreas pancreatic endocrine tumor pancreatic endocrine tumour neuroendocrine tumour of pancreas PANET islet cell tumors - pancreas well differentiated pancreatic endocrine tumour pancreatic neuroendocrine tumor well-differentiated pancreatic NEN islet cell tumours of the pancreas Islet cell tumors of the pancreas islet cell tumours - pancreas well-differentiated NEN of pancreas well-differentiated pancreatic neuroendocrine neoplasm islet cell tumors of the pancreas well-differentiated neuroendocrine neoplasm of pancreas well differentiated pancreatic endocrine neoplasm islet cell tumor pancreatic NET well differentiated pancreatic endocrine tumor islet cell tumour |
|
| Definitions |
A low or intermediate grade well differentiated tumor with neuroendocrine differentiation that arises from the pancreas. According to the presence or absence of clinical syndromes that result from hormone hypersecretion, pancreatic neuroendocrine tumors are classified either as functional or nonfunctional Pancreatic endocrine tumor, also known as pancreatic neuroendocrine tumor (PNET), describes a group of endocrine tumors originating in the pancreas that are usually indolent and benign, but may have the potential to be malignant. They can be functional, exhibiting a hormonal hypersecretion syndrome, but can be non-functional presenting with non-specific symptoms and include insulinoma, glucagonoma, VIPoma, somatostatinoma (SSoma), PPoma and Zollinger-Ellison syndrome (ZES, or gastrinoma) and other ectopic hormone producing tumors (such as GRFoma). |
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| ID |
http://www.ebi.ac.uk/efo/EFO_1000045 |
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| database_cross_reference |
ICDO:8150/1 NCIT:C27720 NCIt:C27720 Orphanet:97253 MedDRA:10067518 ONCOTREE:PANET UMLS:C1337011 DOID:1799 GARD:13034 MONDO:0019954 |
|
| definition |
A low or intermediate grade well differentiated tumor with neuroendocrine differentiation that arises from the pancreas. According to the presence or absence of clinical syndromes that result from hormone hypersecretion, pancreatic neuroendocrine tumors are classified either as functional or nonfunctional Pancreatic endocrine tumor, also known as pancreatic neuroendocrine tumor (PNET), describes a group of endocrine tumors originating in the pancreas that are usually indolent and benign, but may have the potential to be malignant. They can be functional, exhibiting a hormonal hypersecretion syndrome, but can be non-functional presenting with non-specific symptoms and include insulinoma, glucagonoma, VIPoma, somatostatinoma (SSoma), PPoma and Zollinger-Ellison syndrome (ZES, or gastrinoma) and other ectopic hormone producing tumors (such as GRFoma). |
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| exactMatch | ||
| gwas_trait |
true |
|
| has_exact_synonym |
islet cell tumors - pancreas well differentiated pancreatic endocrine tumour pancreatic neuroendocrine tumor well-differentiated pancreatic NEN islet cell tumours of the pancreas Islet cell tumors of the pancreas islet cell tumours - pancreas well-differentiated NEN of pancreas well-differentiated pancreatic neuroendocrine neoplasm islet cell tumors of the pancreas well-differentiated neuroendocrine neoplasm of pancreas well differentiated pancreatic endocrine neoplasm islet cell tumor pancreatic NET well differentiated pancreatic endocrine tumor islet cell tumour |
|
| has_related_synonym |
neuroendocrine tumor of pancreas pancreatic endocrine tumor pancreatic endocrine tumour neuroendocrine tumour of pancreas PANET |
|
| id |
EFO:1000045 |
|
| in_subset |
http://purl.obolibrary.org/obo/mondo/mondo-base#rare http://purl.obolibrary.org/obo/mondo/mondo-base#otar http://purl.obolibrary.org/obo/mondo/mondo-base#gard_rare http://purl.obolibrary.org/obo/mondo/mondo-base#ordo_group_of_disorders http://purl.obolibrary.org/obo/mondo/mondo-base#disease_grouping |
|
| label |
pancreatic neuroendocrine tumor |
|
| notation |
EFO:1000045 |
|
| preferred label |
pancreatic neuroendocrine tumor |
|
| prefLabel |
pancreatic neuroendocrine tumor |
|
| term editor |
Laura Huerta |
|
| subClassOf |