loading...| Preferred Name | Primary progressive aphasia | |
| Synonyms |
primary progressive aphasia syndrome Mesulam syndrome primary progressive aphasia PPA |
|
| Definitions |
Primary progressive aphasia (PPA) is a neurodegenerative disorder, characterized by a primary dissolution of language, with relative sparing of other mental faculties for at least the first 2 years of illness. PPA is recognized as the language variant in the frontotemporal dementia (FTD) spectrum of disorders. PPA can be classified into 3 subtypes based on specific speech and language features: semantic dementia (SD), progressive non-fluent aphasia (PNFA) and logopenic progressive aphasia (lv-PPA). |
|
| ID |
http://www.ebi.ac.uk/efo/EFO_0009053 |
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| database_cross_reference |
NCIT:C85024 Orphanet:95432 MeSH:D018888 MedDRA:10081268 DOID:0081388 UMLS:C0282513 MONDO:0019806 MEDGEN:79466 MESH:D018888 GARD:8541 |
|
| definition |
Primary progressive aphasia (PPA) is a neurodegenerative disorder, characterized by a primary dissolution of language, with relative sparing of other mental faculties for at least the first 2 years of illness. PPA is recognized as the language variant in the frontotemporal dementia (FTD) spectrum of disorders. PPA can be classified into 3 subtypes based on specific speech and language features: semantic dementia (SD), progressive non-fluent aphasia (PNFA) and logopenic progressive aphasia (lv-PPA). |
|
| exactMatch |
http://identifiers.org/medgen/79466 http://purl.obolibrary.org/obo/Orphanet_95432 http://purl.obolibrary.org/obo/EFO_0009053 http://purl.obolibrary.org/obo/DOID_0081388 http://linkedlifedata.com/resource/umls/id/C0282513 |
|
| has_exact_synonym |
Mesulam syndrome primary progressive aphasia PPA |
|
| has_related_synonym |
primary progressive aphasia syndrome |
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| IAO_0000233 | ||
| id |
EFO:0009053 |
|
| in_subset |
http://purl.obolibrary.org/obo/mondo/mondo-base#rare http://purl.obolibrary.org/obo/mondo/mondo-base#otar http://purl.obolibrary.org/obo/mondo/mondo-base#gard_rare http://purl.obolibrary.org/obo/mondo/mondo-base#ordo_group_of_disorders http://purl.obolibrary.org/obo/mondo/mondo-base#disease_grouping |
|
| label |
Primary progressive aphasia |
|
| notation |
EFO:0009053 |
|
| preferred label |
Primary progressive aphasia |
|
| prefLabel |
Primary progressive aphasia |
|
| term editor |
Hannah McLaren |
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| subClassOf |