loading...| Preferred Name |
pulmonary arterial hypertension |
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| Synonyms |
PAH pulmonary arterial hypertension PPH idiopathic pulmonary hypertension PAH with overt features of venous/capillaries involvement PVOD/PCH |
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| Definitions |
Pulmonary arterial hypertension (PAH) is a group of diseases characterized by mean pulmonary artery pressure >20 mmHg and elevated pulmonary arterial resistance leading to right heart failure. PAH is progressive and potentially fatal. PAH may be idiopathic and/ or familial, have overt features of venous/capillary involvement (pulmonary veno-occlusive disease, PVOD/pulmonary capillary hemangiomatosis, PCH), induced by drug or toxin (drug-or toxin-induced PAH), or associated with other diseases like congenital heart disease, connective tissue disease, HIV, schistosomiasis, portal hypertension (PAH associated with other disease). |
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| ID |
http://purl.obolibrary.org/obo/MONDO_0015924 |
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| has characteristic | ||
| has_exact_synonym |
PAH pulmonary arterial hypertension |
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| has_narrow_synonym |
PAH with overt features of venous/capillaries involvement PVOD/PCH |
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| has_related_synonym |
PPH idiopathic pulmonary hypertension |
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| IAO_0000233 | ||
| label |
pulmonary arterial hypertension |
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| prefixIRI |
MONDO:0015924 |
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| prefLabel |
pulmonary arterial hypertension |
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| textual definition |
Pulmonary arterial hypertension (PAH) is a group of diseases characterized by mean pulmonary artery pressure >20 mmHg and elevated pulmonary arterial resistance leading to right heart failure. PAH is progressive and potentially fatal. PAH may be idiopathic and/ or familial, have overt features of venous/capillary involvement (pulmonary veno-occlusive disease, PVOD/pulmonary capillary hemangiomatosis, PCH), induced by drug or toxin (drug-or toxin-induced PAH), or associated with other diseases like congenital heart disease, connective tissue disease, HIV, schistosomiasis, portal hypertension (PAH associated with other disease). |
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| subClassOf |