Preferred Name |
granulomatosis with polyangiitis |
|
Synonyms |
Wegener's syndrome Wegener's granulomatosis pauci-immune glomerulonephritis associated with granulomatosis with polyangiitis GPA Wegener granulomatosis granulomatosis - Wegener's granulomatosis with polyangiitis necrotizing respiratory granulomatosis ANCA-associated vasculitis Wg Midline granulomatosis |
|
Definitions |
A small-vessel necrotizing vasculitis characterised by the association of inflammation of the vessel wall and peri- and extravascular granulomatosis. |
|
ID |
http://purl.obolibrary.org/obo/MONDO_0012105 |
|
has_broad_synonym |
ANCA-associated vasculitis Wg |
|
has_exact_synonym |
Wegener's syndrome Wegener's granulomatosis pauci-immune glomerulonephritis associated with granulomatosis with polyangiitis GPA Wegener granulomatosis granulomatosis - Wegener's granulomatosis with polyangiitis necrotizing respiratory granulomatosis |
|
has_related_synonym |
Midline granulomatosis |
|
IAO_0000233 | ||
label |
granulomatosis with polyangiitis |
|
prefixIRI |
MONDO:0012105 |
|
prefLabel |
granulomatosis with polyangiitis |
|
textual definition |
A small-vessel necrotizing vasculitis characterised by the association of inflammation of the vessel wall and peri- and extravascular granulomatosis. |
|
subClassOf |
http://purl.obolibrary.org/obo/MONDO_0015492 http://purl.obolibrary.org/obo/MONDO_0002462 |