Preferred Name

Kasabach-Merritt syndrome

Synonyms

Kasabach-Merritt syndrome

hemangioma-hemorrhage syndrome

hemangioma-thrombocytopenia syndrome

thrombocytopenia-hemangioma syndrome

hemangiomatosis with thrombocytopenia

thrombopenia-hemangioma syndrome

hemangioma thrombocytopenia syndrome

Kasabach Merritt phenomenon

Kasabach Merritt syndrome

KMP

Definitions

Kasabach-Merritt syndrome (KMS), also known as hemangioma-thrombocytopenia syndrome, is a rare disorder characterized by profound thrombocytopenia, microangiopathic hemolytic anemia, and subsequent consumptive coagulopathy in association with vascular tumors, particularly kaposiform hemangioendothelioma or tufted angioma.

ID

http://purl.obolibrary.org/obo/MONDO_0007708

has_exact_synonym

Kasabach-Merritt syndrome

hemangioma-hemorrhage syndrome

hemangioma-thrombocytopenia syndrome

thrombocytopenia-hemangioma syndrome

hemangiomatosis with thrombocytopenia

thrombopenia-hemangioma syndrome

has_related_synonym

hemangioma thrombocytopenia syndrome

Kasabach Merritt phenomenon

Kasabach Merritt syndrome

KMP

label

Kasabach-Merritt syndrome

prefixIRI

MONDO:0007708

prefLabel

Kasabach-Merritt syndrome

textual definition

Kasabach-Merritt syndrome (KMS), also known as hemangioma-thrombocytopenia syndrome, is a rare disorder characterized by profound thrombocytopenia, microangiopathic hemolytic anemia, and subsequent consumptive coagulopathy in association with vascular tumors, particularly kaposiform hemangioendothelioma or tufted angioma.

subClassOf

http://purl.obolibrary.org/obo/MONDO_0003847

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