Preferred Name |
primary biliary cholangitis |
|
Synonyms |
Hanot syndrome primary biliary cirrhosis biliary liver cirrhosis primary Bilary cirrhosis (PBC) PBC chronic non-suppurative destructive cholangitis chronic nonsuppurative destructive cholangitis cholestatic cirrhosis familial primary biliary cirrhosis biliary cirrhosis, primary |
|
Definitions |
Primary biliary cholangitis (PBC) is a chronic and slowly progressive cholestatic liver disease of autoimmune etiology characterized by injury of the intrahepatic bile ducts that may eventually lead to liver failure. |
|
ID |
http://purl.obolibrary.org/obo/MONDO_0005388 |
|
has_exact_synonym |
Hanot syndrome primary biliary cirrhosis biliary liver cirrhosis primary Bilary cirrhosis (PBC) PBC chronic non-suppurative destructive cholangitis chronic nonsuppurative destructive cholangitis cholestatic cirrhosis |
|
has_related_synonym |
familial primary biliary cirrhosis biliary cirrhosis, primary |
|
label |
primary biliary cholangitis |
|
prefixIRI |
MONDO:0005388 |
|
prefLabel |
primary biliary cholangitis |
|
textual definition |
Primary biliary cholangitis (PBC) is a chronic and slowly progressive cholestatic liver disease of autoimmune etiology characterized by injury of the intrahepatic bile ducts that may eventually lead to liver failure. |
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subClassOf |