Preferred Name |
essential thrombocythemia |
|
Synonyms |
essential thrombocythaemia essential thrombocythemia hemorrhagic thrombocythemia essential thrombocytosis primary thrombocytosis primary thrombocythemia essential thrombocytemia ET idiopathic thrombocythemia |
|
Definitions |
A chronic myeloproliferative neoplasm that involves primarily the megakaryocytic lineage. It is characterized by sustained thrombocytosis in the blood, increased numbers of large, mature megakaryocytes in the bone marrow, and episodes of thrombosis and/or hemorrhage. (WHO, 2008) |
|
ID |
http://purl.obolibrary.org/obo/MONDO_0005029 |
|
has_broad_synonym |
ET |
|
has_exact_synonym |
essential thrombocythaemia essential thrombocythemia hemorrhagic thrombocythemia essential thrombocytosis primary thrombocytosis primary thrombocythemia essential thrombocytemia |
|
has_narrow_synonym |
idiopathic thrombocythemia |
|
IAO_0000233 | ||
label |
essential thrombocythemia |
|
prefixIRI |
MONDO:0005029 |
|
prefLabel |
essential thrombocythemia |
|
seeAlso |
https://rarediseases.info.nih.gov/diseases/6594/essential-thrombocythemia |
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textual definition |
A chronic myeloproliferative neoplasm that involves primarily the megakaryocytic lineage. It is characterized by sustained thrombocytosis in the blood, increased numbers of large, mature megakaryocytes in the bone marrow, and episodes of thrombosis and/or hemorrhage. (WHO, 2008) |
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subClassOf |