Preferred Name |
carglumic acid |
|
Synonyms |
Carbamylglutamic acid N-carbamoyl-L-glutamic acid acido carglumico L-N-Carbamoylglutamic acid (2S)-2-(carbamoylamino)pentanedioic acid Ureidoglutaric acid acide carglumique Carbamino-L-glutamic acid C6H10N2O5 acidum carglumicum Carbaglu carglumic acid |
|
ID |
http://purl.obolibrary.org/obo/CHEBI_71028 |
|
AHFScode |
40:10 |
|
ATCCode |
A16AA05 |
|
CASRN |
1188-38-1 |
|
DBBrand |
carbaglu |
|
DBname |
carglumic acid |
|
DBSynonym |
n-carbamoyl-l-glutamic acid n-carbamyl-l-glutamate (s)-2-ureidopentanedioic acid n-carbamylglutamate |
|
Definition |
A urea that is the N-carbamoyl derivative of L-glutamic acid. An orphan drug used to treat a deficiency in the enzyme N-acetylglutamate synthase, which leads to acute hyperammonaemia. |
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has pharmacological target | ||
has role | ||
InChI |
InChI=1S/C6H10N2O5/c7-6(13)8-3(5(11)12)1-2-4(9)10/h3H,1-2H2,(H,9,10)(H,11,12)(H3,7,8,13)/t3-/m0/s1 |
|
InChIKey |
InChIKey=LCQLHJZYVOQKHU-VKHMYHEASA-N |
|
label |
carglumic acid |
|
prefixIRI |
obo2:CHEBI_71028 |
|
prefLabel |
carglumic acid |
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related with | ||
SMILES |
NC(=O)N[C@@H](CCC(O)=O)C(O)=O |
|
Synonym |
Carbamylglutamic acid N-carbamoyl-L-glutamic acid acido carglumico L-N-Carbamoylglutamic acid (2S)-2-(carbamoylamino)pentanedioic acid Ureidoglutaric acid acide carglumique Carbamino-L-glutamic acid C6H10N2O5 acidum carglumicum Carbaglu carglumic acid |
|
xref |
Reaxys:1727929 National Drug Code Directory:52276-312-05 CiteXplore:20410539 PubChem Compound:121396 CiteXplore:22858088 ChEBI:71028 ChemSpider:108351 Wikipedia:Carglumic_acid KEGG DRUG:D07130 CASRN:1188-38-1 CiteXplore:17421020 CiteXplore:21941437 CiteXplore:21225012 DrugBank:DB06775 PubChem Substance:99443290 Wikipedia:http://en.wikipedia.org/wiki/Carglumic_acid CiteXplore:18516804 Drugs.com:http://www.drugs.com/carbaglu.html HMDB:HMDB15673 KEGG COMPOUND:C05829 CiteXplore:18604903 PharmGKB:PA165958402 RxList:http://www.rxlist.com/carbaglu-drug.htm MetaCyc:N-CARBAMYL-L-GLUTAMATE CiteXplore:21207059 ChEMBL:775731 CiteXplore:18234091 CiteXplore:15055204 CiteXplore:21403788 |
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subClassOf |