Preferred Name | Paraganglioma | |
Synonyms |
chemodectoma tumour of the paraganglion neoplasm of the paraganglion paraganglioma tumor of the paraganglion paraganglion tumor tumor of paraganglion paragangliomas neoplasm of paraganglion paraganglion tumour Paraganglionic neoplasm paraganglion neoplasm Paraganglionic tumour Paraganglionic tumor tumour of paraganglion |
|
Definitions |
A benign or malignant neoplasm arising from paraganglia located along the sympathetic or parasympathetic nerves. Infrequently, it may arise outside the usual distribution of the sympathetic and parasympathetic paraganglia. Tumors arising from the adrenal gland medulla are called pheochromocytomas. Morphologically, paragangliomas usually display a nesting (Zellballen) growth pattern. There are no reliable morphologic criteria to distinguish between benign and malignant paragangliomas. The only definitive indicator of malignancy is the presence of regional or distant metastases. |
|
ID |
http://www.ebi.ac.uk/efo/EFO_1000453 |
|
database_cross_reference |
OMIM:618464 MedDRA:10073860 DOID:0050773 OMIM:618475 UMLS:C0030421 MESH:D010235 ICDO:8680/1 MONDO:0000448 OMIMPS:168000 MEDGEN:10571 SCTID:127027008 ONCOTREE:PGNG ICD9:239.7 NCIT:C3308 NCIt:C3308 |
|
definition |
A benign or malignant neoplasm arising from paraganglia located along the sympathetic or parasympathetic nerves. Infrequently, it may arise outside the usual distribution of the sympathetic and parasympathetic paraganglia. Tumors arising from the adrenal gland medulla are called pheochromocytomas. Morphologically, paragangliomas usually display a nesting (Zellballen) growth pattern. There are no reliable morphologic criteria to distinguish between benign and malignant paragangliomas. The only definitive indicator of malignancy is the presence of regional or distant metastases. |
|
has_exact_synonym |
tumour of the paraganglion neoplasm of the paraganglion paraganglioma tumor of the paraganglion paraganglion tumor tumor of paraganglion paragangliomas neoplasm of paraganglion paraganglion tumour Paraganglionic neoplasm paraganglion neoplasm Paraganglionic tumour Paraganglionic tumor tumour of paraganglion |
|
has_narrow_synonym |
chemodectoma |
|
IAO_0000233 | ||
id |
EFO:1000453 |
|
in_subset |
http://purl.obolibrary.org/obo/mondo/mondo-base#rare |
|
label |
Paraganglioma |
|
notation |
EFO:1000453 |
|
preferred label |
Paraganglioma |
|
prefLabel |
Paraganglioma |
|
skos_exactMatch |
http://identifiers.org/snomedct/127027008 http://purl.obolibrary.org/obo/DOID_0050773 https://omim.org/phenotypicSeries/PS168000 http://linkedlifedata.com/resource/umls/id/C0030421 http://purl.obolibrary.org/obo/EFO_1000453 http://purl.obolibrary.org/obo/NCIT_C3308 |
|
subClassOf |
http://www.ebi.ac.uk/efo/EFO_1001901 http://purl.obolibrary.org/obo/MONDO_0021635 |