Preferred Name

Cysteamine Bitartrate

Synonyms
Definitions

An aminothiol salt used in the treatment of nephropathic cystinosis. Cysteamine bitartrate enters the cell and reacts with cystine producing cysteine and cysteine-cysteamine mixed disulfide compound, both of which, unlike cystine, can pass through the lysosomal membrane. This prevents the accumulation of cystine crystals in the lysosomes of patients with cystinosis, which can cause considerable damage and eventual destruction of the cells, particularly in the kidneys. (NCI05)

ID

http://purl.obolibrary.org/obo/NCIT_C47467

CAS_Registry

27761-19-9

CHEBI_ID

CHEBI:50386

Chemical_Formula

C4H6O6.C2H7NS

code

C47467

Contributing_Source

FDA

definition

An aminothiol salt used in the treatment of nephropathic cystinosis. Cysteamine bitartrate enters the cell and reacts with cystine producing cysteine and cysteine-cysteamine mixed disulfide compound, both of which, unlike cystine, can pass through the lysosomal membrane. This prevents the accumulation of cystine crystals in the lysosomes of patients with cystinosis, which can cause considerable damage and eventual destruction of the cells, particularly in the kidneys. (NCI05)

FDA_UNII_Code

QO84GZ3TST

Has_Free_Acid_Or_Base_Form

http://purl.obolibrary.org/obo/NCIT_C61696

in_subset

http://purl.obolibrary.org/obo/NCIT_C63923

label

Cysteamine Bitartrate

Legacy Concept Name

Cysteamine_Bitartrate

Preferred_Name

Cysteamine Bitartrate

prefixIRI

NCIT:C47467

prefLabel

Cysteamine Bitartrate

Semantic_Type

Pharmacologic Substance

UMLS_CUI

C0282119

subClassOf

http://purl.obolibrary.org/obo/NCIT_C29701

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