loading...| Preferred Name |
Lymphomatoid Papulosis |
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| Synonyms |
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| Definitions |
A chronic, recurrent cutaneous disorder characterized by the presence of spontaneously regressing papules. The papules are composed of an atypical lymphocytic infiltrate that contains anaplastic CD30-positive T-cells, which are found in type A and diffuse large cell type (type C) lymphomatoid papulosis. In a small number of cases, of type B, the lymphocytic infiltrate is composed of small, cerebriform-like lymphocytes that are often negative for CD30. The majority of cases follow a benign clinical course, but some cases are clonal and may progress to lymphoma. Treatment options include low dose methotrexate and psoralen/UVA (PUVA). |
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| ID |
http://purl.obolibrary.org/obo/NCIT_C3721 |
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| code |
C3721 |
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| Contributing_Source |
GDC |
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| definition |
A chronic, recurrent cutaneous disorder characterized by the presence of spontaneously regressing papules. The papules are composed of an atypical lymphocytic infiltrate that contains anaplastic CD30-positive T-cells, which are found in type A and diffuse large cell type (type C) lymphomatoid papulosis. In a small number of cases, of type B, the lymphocytic infiltrate is composed of small, cerebriform-like lymphocytes that are often negative for CD30. The majority of cases follow a benign clinical course, but some cases are clonal and may progress to lymphoma. Treatment options include low dose methotrexate and psoralen/UVA (PUVA). |
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| ICD-O-3_Code |
9718/1 |
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| in_subset |
http://purl.obolibrary.org/obo/NCIT_C177537 |
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| Is_Value_For_GDC_Property | ||
| label |
Lymphomatoid Papulosis |
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| Legacy Concept Name |
Lymphomatoid_Papulosis |
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| Maps_To |
Lymphomatoid papulosis 9718/3 |
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| Neoplastic_Status |
Uncertain Malignant Potential |
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| Preferred_Name |
Lymphomatoid Papulosis |
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| prefixIRI |
NCIT:C3721 |
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| prefLabel |
Lymphomatoid Papulosis |
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| Semantic_Type |
Neoplastic Process |
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| UMLS_CUI |
C0206182 |
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| subClassOf |
http://purl.obolibrary.org/obo/NCIT_C27897 |