loading...| Preferred Name |
Granulomatosis with Polyangiitis |
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| Synonyms |
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| Definitions |
A rare, autoimmune, systemic medium and small size vasculitis. It is characterized by the formation of necrotizing granulomas in the respiratory tract, necrotizing angiitis, and glomerulonephritis. |
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| ID |
http://purl.obolibrary.org/obo/NCIT_C3444 |
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| ALT_DEFINITION |
Systemic vasculitis affecting small to medium-sized vessels, characterized by necrotizing granulomas in the respiratory tract, necrotizing angiitis, glomerulonephritis with little to no immune complex deposition, and typically positive for antineutrophil cytoplasmic antibody staining in a cytoplasmic pattern (C-ANCA; antiproteinase 3). |
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| code |
C3444 |
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| Contributing_Source |
Cellosaurus NICHD |
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| definition |
A rare, autoimmune, systemic medium and small size vasculitis. It is characterized by the formation of necrotizing granulomas in the respiratory tract, necrotizing angiitis, and glomerulonephritis. |
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| in_subset |
http://purl.obolibrary.org/obo/NCIT_C90259 |
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| label |
Granulomatosis with Polyangiitis |
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| Legacy Concept Name |
Wegener_s_Granulomatosis |
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| Preferred_Name |
Granulomatosis with Polyangiitis |
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| prefixIRI |
NCIT:C3444 |
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| prefLabel |
Granulomatosis with Polyangiitis |
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| Semantic_Type |
Disease or Syndrome |
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| UMLS_CUI |
C3495801 |
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| subClassOf |
http://purl.obolibrary.org/obo/NCIT_C35317 |