loading...| Preferred Name |
Myofibromatosis |
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| Synonyms |
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| Definitions |
A mesenchymal neoplasm characterized by solitary or multiple nodules involving the skin, striated muscles, bones and, sometimes, viscera. It usually appears as a subcutaneous nodule, but can also appear as an ulcer, pedunculated lesion, or similar to a hemangioma. Histology shows well-circumscribed tapered cell lobes, resembling smooth muscle cells. At its center, perivascular round cells (hemangiopericitoides) are usually observed, giving a biphasic appearance. |
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| ID |
http://purl.obolibrary.org/obo/HP_0020135 |
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| creation date |
2019-07-05T17:28:59Z |
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| creator | ||
| definition |
A mesenchymal neoplasm characterized by solitary or multiple nodules involving the skin, striated muscles, bones and, sometimes, viscera. It usually appears as a subcutaneous nodule, but can also appear as an ulcer, pedunculated lesion, or similar to a hemangioma. Histology shows well-circumscribed tapered cell lobes, resembling smooth muscle cells. At its center, perivascular round cells (hemangiopericitoides) are usually observed, giving a biphasic appearance. |
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| label |
Myofibromatosis |
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| prefixIRI |
HP:0020135 |
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| prefLabel |
Myofibromatosis |
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| subClassOf |