SNOMED CT, US Edition

Last uploaded: March 22, 2026
Id http://purl.bioontology.org/ontology/SNOMEDCT/770667002
http://purl.bioontology.org/ontology/SNOMEDCT/770667002
Preferred Name

Occult macular dystrophy

Definitions
Occult macular dystrophy is a rare, genetic retinal dystrophy disease characterised by bilateral progressive decline of visual acuity, due to retinal dysfunction confined only to the macula, associated with normal fundus and fluorescein angiograms and severly attenuated focal macular and multifocal electroretinograms. Occult macular dystrophy is a rare, genetic retinal dystrophy disease characterized by bilateral progressive decline of visual acuity, due to retinal dysfunction confined only to the macula, associated with normal fundus and fluorescein angiograms and severly attenuated focal macular and multifocal electroretinograms. A rare genetic retinal dystrophy disease with characteristics of bilateral progressive decline of visual acuity due to retinal dysfunction confined only to the macula, associated with normal fundus and fluorescein angiograms and severly attenuated focal macular and multifocal electroretinograms. There is evidence the disease is caused by heterozygous mutation in the RP1L1 gene on chromosome 8p23.
Synonyms
Occult macular dystrophy (disorder)
OMD - occult macular dystrophy
OCMD - occult macular dystrophy
Type http://www.w3.org/2002/07/owl#Class
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