SNOMED CT, US Edition

Last uploaded: March 22, 2026
Id http://purl.bioontology.org/ontology/SNOMEDCT/724838009
http://purl.bioontology.org/ontology/SNOMEDCT/724838009
Preferred Name

Hereditary skin peeling syndrome

Definitions
A group of rare autosomal recessive forms of ichthyosis with clinical characteristics of superficial, asymptomatic, spontaneous peeling of the skin and histologically by a shedding of the outer layers of the epidermis. Presents with either an acral or a generalized distribution. A group of rare autosomal recessive forms of ichthyosis with clinical characteristics of superficial, asymptomatic, spontaneous peeling of the skin and histologically by a shedding of the outer layers of the epidermis. Presents with either an acral or a generalised distribution. A group of rare autosomal recessive forms of ichthyosis clinically characterized by superficial, asymptomatic, spontaneous peeling of the skin and histologically by a shedding of the outer layers of the epidermis. PSS presents with either an acral (acral PSS) or a generalized distribution for generalized PSS type A (noninflammatory) or B (inflammatory). A group of rare autosomal recessive forms of ichthyosis clinically characterised by superficial, asymptomatic, spontaneous peeling of the skin and histologically by a shedding of the outer layers of the epidermis. PSS presents with either an acral (acral PSS) or a generalised distribution for generalised PSS type A (noninflammatory) or B (inflammatory).
Synonyms
Peeling skin syndrome
Hereditary skin peeling syndrome (disorder)
Familial continuous skin peeling syndrome
Type http://www.w3.org/2002/07/owl#Class
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