Preferred Name |
Arrhythmogenic Right Ventricular Dysplasia |
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Synonyms |
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|
Definitions |
An intrinsic cardiomyopathy that is characterized by hypokinetic areas involving the free wall of the right ventricle, with fibrofatty replacement of the right ventricular myocardium, with associated arrhythmias originating in the right ventricle. |
|
ID |
http://www.phoc.org.cn/pmo/class/PMO_00036207 |
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Database_Cross_Reference |
MTH:NOCODE MEDCIN:315764 NDFRT:N0000003938 DO:DOID:0050431 MSH:D019571 NCI:C84571 MDR:10058093 RCD:X77yR OMIM:MTHU006085 SNOMEDCT_VET:281170005 SNOMEDCT_US:281170005 RCD:Xa1fq SNOMEDCT_US:253528005 |
|
Definition |
An intrinsic cardiomyopathy that is characterized by hypokinetic areas involving the free wall of the right ventricle, with fibrofatty replacement of the right ventricular myocardium, with associated arrhythmias originating in the right ventricle. |
|
label |
Arrhythmogenic Right Ventricular Dysplasia |
|
MCID |
MC00125317 |
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PMOID |
PMO:00036207 |
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prefixIRI |
pmo:PMO_00036207 |
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prefLabel |
Arrhythmogenic Right Ventricular Dysplasia |
|
Synonym |
Arrythmogenic right ventricular dysplasia (disorder) Arrhythmogenic Right Ventricular Dysplasia-Cardiomyopathy Arrythmogenic right ventricular dysplasia Arrhy right ventric cardiomyop Arrhythmogenic Right Ventricular Cardiomyopathy Arrhythmogenic right ventricular cardiomyopathy arrhythmogenic right ventricular dysplasia/cardiomyopathy Arrhythmogenic right ventricular dysplasia ARVC cardiomyopathy Arrhythmogenic Right Ventricular Cardiomyopathy-Dysplasia Arrythmogen rt vent dysplasia Arrhythmogenic Right Ventricular Cardiomyopathy Dysplasia ARVD Ventricular Dysplasia, Right, Arrhythmogenic ARVD-C Boxer cardiomyopathy arrhythmogenic right ventricular cardiomyopathy ARVC Arrhythmogenic Right Ventricular Dysplasia [Disease/Finding] arrhythmogenic right ventricular dysplasia arrhythmogenic right ventricular dysplasia (diagnosis) Arrhythmogenic right ventricular dysplasia (disorder) Arrhythm right ventric dysplas Right Ventricular Dysplasia, Arrhythmogenic Arrhythmogenic right ventricular cardiomyopathy (disorder) Arrhythmogenic RVD Right Ventricular Dysplasia |
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Tree Number |
T9.20.1.10.1 T9.8.3.3.1.22 T9.20.1.3.22 T9.20.3.1.22 |
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subClassOf |
http://www.phoc.org.cn/pmo/class/PMO_00004451 http://www.phoc.org.cn/pmo/class/PMO_00004627 |