PMO Precision Medicine Ontology

Last uploaded: December 16, 2020
Preferred Name

Arrhythmogenic Right Ventricular Dysplasia

Synonyms
Definitions

An intrinsic cardiomyopathy that is characterized by hypokinetic areas involving the free wall of the right ventricle, with fibrofatty replacement of the right ventricular myocardium, with associated arrhythmias originating in the right ventricle.

ID

http://www.phoc.org.cn/pmo/class/PMO_00036207

Database_Cross_Reference

MTH:NOCODE

MEDCIN:315764

NDFRT:N0000003938

DO:DOID:0050431

MSH:D019571

NCI:C84571

MDR:10058093

RCD:X77yR

OMIM:MTHU006085

SNOMEDCT_VET:281170005

SNOMEDCT_US:281170005

RCD:Xa1fq

SNOMEDCT_US:253528005

Definition

An intrinsic cardiomyopathy that is characterized by hypokinetic areas involving the free wall of the right ventricle, with fibrofatty replacement of the right ventricular myocardium, with associated arrhythmias originating in the right ventricle.

label

Arrhythmogenic Right Ventricular Dysplasia

MCID

MC00125317

PMOID

PMO:00036207

prefixIRI

pmo:PMO_00036207

prefLabel

Arrhythmogenic Right Ventricular Dysplasia

Synonym

Arrythmogenic right ventricular dysplasia (disorder)

Arrhythmogenic Right Ventricular Dysplasia-Cardiomyopathy

Arrythmogenic right ventricular dysplasia

Arrhy right ventric cardiomyop

Arrhythmogenic Right Ventricular Cardiomyopathy

Arrhythmogenic right ventricular cardiomyopathy

arrhythmogenic right ventricular dysplasia/cardiomyopathy

Arrhythmogenic right ventricular dysplasia

ARVC cardiomyopathy

Arrhythmogenic Right Ventricular Cardiomyopathy-Dysplasia

Arrythmogen rt vent dysplasia

Arrhythmogenic Right Ventricular Cardiomyopathy Dysplasia

ARVD

Ventricular Dysplasia, Right, Arrhythmogenic

ARVD-C

Boxer cardiomyopathy

arrhythmogenic right ventricular cardiomyopathy

ARVC

Arrhythmogenic Right Ventricular Dysplasia [Disease/Finding]

arrhythmogenic right ventricular dysplasia

arrhythmogenic right ventricular dysplasia (diagnosis)

Arrhythmogenic right ventricular dysplasia (disorder)

Arrhythm right ventric dysplas

Right Ventricular Dysplasia, Arrhythmogenic

Arrhythmogenic right ventricular cardiomyopathy (disorder)

Arrhythmogenic RVD

Right Ventricular Dysplasia

Tree Number

T9.20.1.10.1

T9.8.3.3.1.22

T9.20.1.3.22

T9.20.3.1.22

subClassOf

http://www.phoc.org.cn/pmo/class/PMO_00004451

http://www.phoc.org.cn/pmo/class/PMO_00004627

http://www.phoc.org.cn/pmo/class/PMO_00036216

http://www.phoc.org.cn/pmo/class/PMO_00036206

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