Preferred Name |
Total_Colonic_Aganglionosis |
|
Synonyms |
|
|
ID |
http://www.owl-ontologies.com/Ontology1358660052.owl#Total_Colonic_Aganglionosis |
|
ID |
C101040 |
|
NCI_Definition |
The severe form of Hirschsprung disease, this is characterized by a complete lack of nerve cells in the large intestine, and often a partial lack in the small intestine. The bowel is not stimulated without innervation and obstruction ensues. Surgical intervention is necessary. |
|
NCI_PT |
Total Colonic Aganglionosis |
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NICHD_Definition |
_ |
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prefixIRI |
Total_Colonic_Aganglionosis |
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prefLabel |
Total_Colonic_Aganglionosis |
|
Subset_Association1 |
NICHD Pediatric Terminology |
|
Subset_Association2 |
Neonatal Research Network Terminology |
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SYN | ||
subClassOf |
http://www.owl-ontologies.com/Ontology1358660052.owl#Total_Intestinal_Aganglionosis |
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