Pediatric Terminology

Last uploaded: January 25, 2013
Preferred Name

Total_Colonic_Aganglionosis

Synonyms
ID

http://www.owl-ontologies.com/Ontology1358660052.owl#Total_Colonic_Aganglionosis

ID

C101040

NCI_Definition

The severe form of Hirschsprung disease, this is characterized by a complete lack of nerve cells in the large intestine, and often a partial lack in the small intestine. The bowel is not stimulated without innervation and obstruction ensues. Surgical intervention is necessary.

NCI_PT

Total Colonic Aganglionosis

NICHD_Definition

_

prefixIRI

Total_Colonic_Aganglionosis

prefLabel

Total_Colonic_Aganglionosis

Subset_Association1

NICHD Pediatric Terminology

Subset_Association2

Neonatal Research Network Terminology

SYN

subClassOf

http://www.owl-ontologies.com/Ontology1358660052.owl#Total_Intestinal_Aganglionosis

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