Preferred Name |
Histiocytic_Syndrome |
|
Synonyms |
|
|
ID |
http://www.owl-ontologies.com/Ontology1358660052.owl#Histiocytic_Syndrome |
|
ID |
C3107 |
|
NCI_Definition |
A neoplastic proliferation of Langerhans cells which contain Birbeck granules by ultrastructural examination. Three major overlapping syndromes are recognized: eosinophilic granuloma, Letterer-Siwe disease, and Hand-Schuller-Christian disease. The clinical course is generally related to the number of organs affected at presentation. (WHO, 2001) |
|
NCI_PT |
Langerhans Cell Histiocytosis |
|
NICHD_Definition |
_ |
|
prefixIRI |
Histiocytic_Syndrome |
|
prefLabel |
Histiocytic_Syndrome |
|
Subset_Association1 |
NICHD Pediatric Terminology |
|
Subset_Association2 |
Neonatal Research Network Terminology |
|
SYN | ||
subClassOf |
http://www.owl-ontologies.com/Ontology1358660052.owl#Neoplasm |
Create mapping
Delete | Mapping To | Ontology | Source |
---|---|---|---|
http://purl.bioontology.org/ontology/SNOMEDCT/127068004 | SNOMEDCT | LOOM | |
http://purl.bioontology.org/ontology/RCD/X20E5 | RCD | LOOM |