Physician Data Query

Last uploaded: January 31, 2024
Preferred Name

dermatofibrosarcoma protuberans

Synonyms

DFSP

Definitions

An intermediate cutaneous fibrohistiocytic neoplasm, presenting as a nodular cutaneous mass, most often on the trunk and the proximal extremities. The tumor diffusely infiltrates the dermis and the subcutaneous tissues. It is considered a locally aggressive neoplasm, which often recurs but rarely metastasizes. Check for "https://www.cancer.gov/about-cancer/treatment/clinical-trials/intervention/C4683" active clinical trials using this agent. ("http://ncit.nci.nih.gov/ncitbrowser/ConceptReport.jsp?dictionary=NCI%20Thesaurus&code=C4683" NCI Thesaurus)

ID

http://purl.bioontology.org/ontology/PDQ/CDR0000474442

altLabel

DFSP

dermatofibrosarcoma

cui

C0206647

C0392784

DATE FIRST PUBLISHED

2006-03-17

Date last modified

2011-06-02

definition

An intermediate cutaneous fibrohistiocytic neoplasm, presenting as a nodular cutaneous mass, most often on the trunk and the proximal extremities. The tumor diffusely infiltrates the dermis and the subcutaneous tissues. It is considered a locally aggressive neoplasm, which often recurs but rarely metastasizes. Check for "https://www.cancer.gov/about-cancer/treatment/clinical-trials/intervention/C4683" active clinical trials using this agent. ("http://ncit.nci.nih.gov/ncitbrowser/ConceptReport.jsp?dictionary=NCI%20Thesaurus&code=C4683" NCI Thesaurus)

NCI ID

C4683

notation

CDR0000474442

ORIG STY

Neoplasm diagnosis

prefLabel

dermatofibrosarcoma protuberans

tui

T191

subClassOf

http://purl.bioontology.org/ontology/PDQ/CDR0000040298

http://purl.bioontology.org/ontology/PDQ/CDR0000040175

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http://purl.bioontology.org/ontology/MDRGER/10057043 MDRGER CUI
http://purl.bioontology.org/ontology/MDRGER/10057070 MDRGER CUI
http://purl.bioontology.org/ontology/MSHFRE/D018223 MSHFRE CUI
http://purl.bioontology.org/ontology/MEDDRA/10057043 MEDDRA CUI
http://purl.bioontology.org/ontology/RCD/Xa99p RCD CUI
http://purl.bioontology.org/ontology/SNMI/M-88323 SNMI CUI
http://purl.bioontology.org/ontology/MDRFRE/10057043 MDRFRE CUI
http://purl.bioontology.org/ontology/MESH/D018223 MESH CUI
http://purl.bioontology.org/ontology/NDFRT/N0000003697 NDFRT CUI
http://purl.bioontology.org/ontology/CSP/2000-6227 CRISP CUI
http://purl.bioontology.org/ontology/SCTSPA/76594008 SCTSPA CUI
http://purl.bioontology.org/ontology/SNMI/M-88323 SNMI CUI
http://purl.bioontology.org/ontology/SNOMEDCT/76594008 SNOMEDCT CUI
http://purl.bioontology.org/ontology/MEDDRA/10057070 MEDDRA CUI
http://purl.bioontology.org/ontology/RCD/Xa0D9 RCD CUI
http://purl.bioontology.org/ontology/MDRFRE/10057070 MDRFRE CUI
http://purl.bioontology.org/ontology/SNOMEDCT/276799004 SNOMEDCT CUI
http://purl.bioontology.org/ontology/SCTSPA/276799004 SCTSPA CUI
http://purl.obolibrary.org/obo/MONDO_0011934 MONDO LOOM
http://purl.obolibrary.org/obo/DOID_3507 DOID LOOM
rgo:13069 GAMUTS LOOM
rgo:13069 GAMUTS LOOM
http://purl.obolibrary.org/obo/MONDO_0011934 EFO LOOM
http://purl.obolibrary.org/obo/DOID_3507 DOID LOOM
http://www.orpha.net/ORDO/Orphanet_31112 ORDO LOOM
http://sbmi.uth.tmc.edu/ontology/ochv#C0392784 OCHV LOOM
http://purl.obolibrary.org/obo/MONDO_0011934 DOVES LOOM
http://purl.bioontology.org/ontology/RCTV2/B339.00 RCTV2 LOOM
http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C4683 NCIT LOOM
http://purl.obolibrary.org/obo/DERMO_0001155 DERMO LOOM
http://www.owl-ontologies.com/unnamed.owl#RID17036 DERMLEX LOOM
http://purl.bioontology.org/ontology/OMIM/607907 OMIM LOOM
http://purl.bioontology.org/ontology/SNOMEDCT/76594008 SNOMEDCT LOOM
http://purl.bioontology.org/ontology/MEDDRA/10057070 MEDDRA LOOM
http://purl.obolibrary.org/obo/NCIT_C4683 BERO LOOM
http://purl.obolibrary.org/obo/DOID_3507 BAO LOOM
http://purl.obolibrary.org/obo/DOID_3507 HHEAR LOOM
http://purl.obolibrary.org/obo/DOID_3507 ODAE LOOM
http://purl.obolibrary.org/obo/DOID_3507 NIFSTD LOOM
http://purl.obolibrary.org/obo/DOID_3507 MIDO LOOM
http://purl.obolibrary.org/obo/DOID_3507 FNS-H LOOM
http://purl.bioontology.org/ontology/RCD/Xa0D9 RCD LOOM
http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#Dermatofibrosarcoma_Protuberans CSEO LOOM
http://purl.bioontology.org/ontology/SNOMEDCT/276799004 SNOMEDCT LOOM
http://phenomebrowser.net/ontologies/mesh/mesh.owl#C538219 RH-MESH LOOM
http://www.gamuts.net/entity#dermatofibrosarcoma_protuberans GAMUTS LOOM
http://www.limics.org/hrdo/rdfns#pat_id_9285 HRDO LOOM