loading...| Preferred Name |
Neuroendocrine tumor of pancreas |
|
| Synonyms |
Well-differentiated neuroendocrine neoplasm of pancreas PNET Well-differentiated pancreatic NEN Well-differentiated NEN of pancreas Well-differentiated pancreatic neuroendocrine neoplasm Pancreatic NET Pancreatic neuroendocrine tumor |
|
| Definitions |
Pancreatic endocrine tumor, also known as pancreatic neuroendocrine tumor (PNET), describes a group of endocrine tumors originating in the pancreas that are usually indolent and benign, but may have the potential to be malignant. They can be functional, exhibiting a hormonal hypersecretion syndrome, but can be non-functional presenting with non-specific symptoms and include insulinoma, glucagonoma, VIPoma, somatostatinoma (SSoma), PPoma and Zollinger-Ellison syndrome (ZES, or gastrinoma) and other ectopic hormone producing tumors (such as GRFoma) (see these terms). |
|
| ID |
http://www.orpha.net/ORDO/Orphanet_97253 |
|
| alternative_term |
Well-differentiated neuroendocrine neoplasm of pancreas PNET Well-differentiated pancreatic NEN Well-differentiated NEN of pancreas Well-differentiated pancreatic neuroendocrine neoplasm Pancreatic NET Pancreatic neuroendocrine tumor |
|
| definition |
Pancreatic endocrine tumor, also known as pancreatic neuroendocrine tumor (PNET), describes a group of endocrine tumors originating in the pancreas that are usually indolent and benign, but may have the potential to be malignant. They can be functional, exhibiting a hormonal hypersecretion syndrome, but can be non-functional presenting with non-specific symptoms and include insulinoma, glucagonoma, VIPoma, somatostatinoma (SSoma), PPoma and Zollinger-Ellison syndrome (ZES, or gastrinoma) and other ectopic hormone producing tumors (such as GRFoma) (see these terms). |
|
| definition_citation |
Orphanet |
|
| expertlink |
https://www.orpha.net/consor/cgi-bin/OC_Exp.php?Lng=en&Expert=97253 |
|
| has_age_of_onset |
Adult |
|
| has_inheritance |
Not applicable Autosomal dominant |
|
| hasDbXref |
ICD-11:2C10.1 |
|
| label |
Neuroendocrine tumor of pancreas |
|
| notation |
ORPHA:97253 Category |
|
| prefixIRI |
ORDO:Orphanet_97253 |
|
| prefLabel |
Neuroendocrine tumor of pancreas |
|
| present_in |
United States AND has_point_prevalence_average_value : 27.5 AND has_point_prevalence_range : 1-5 / 10 000 Japan AND has_annual_incidence_average_value : 1.27 AND has_annual_incidence_range : 1-9 / 100 000 France AND has_annual_incidence_average_value : 0.21 AND has_annual_incidence_range : 1-9 / 1 000 000 Europe AND has_annual_incidence_average_value : 0.21 AND has_annual_incidence_range : 1-9 / 1 000 000 Europe AND has_point_prevalence_range : 1-5 / 10 000 Japan AND has_point_prevalence_average_value : 2.69 AND has_point_prevalence_range : 1-9 / 100 000 United States AND has_annual_incidence_average_value : 0.22 AND has_annual_incidence_range : 1-9 / 1 000 000 |
|
| subClassOf |
| Delete | Mapping To | Ontology | Source |
|---|---|---|---|
| rgo:04358 | GAMUTS | LOOM | |
| http://purl.bioontology.org/ontology/SNOMEDCT/717919005 | SNOMEDCT | LOOM | |
| http://www.gamuts.net/entity#islet_cell_tumor | GAMUTS | REST |