loading...| Preferred Name | Morvan syndrome | |
| Synonyms |
Limbic encephalitis-neuromyotonia-hyperhidrosis-polyneuropathy syndrome Morvan fibrillary chorea |
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| Definitions |
Morvan syndrome is a rare, life-threatening, acquired neurologic disease characterized by neuromyotonia, dysautonomia and encephalopathy with severe insomnia. Signs involving central (e.g. hallucinations, confusion, amnesia, myoclonus), autonomic (e.g. variations in blood pressure, hyperhidrosis) and peripheral (e.g. painful cramps, myokymia) hyperactivity, as well as systemic manifestations (such as weight loss, pruritus, fever), are reported. Thymoma is present in some cases. |
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| ID |
http://www.orpha.net/ORDO/Orphanet_83467 |
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| alternative_term |
Limbic encephalitis-neuromyotonia-hyperhidrosis-polyneuropathy syndrome Morvan fibrillary chorea |
|
| definition |
Morvan syndrome is a rare, life-threatening, acquired neurologic disease characterized by neuromyotonia, dysautonomia and encephalopathy with severe insomnia. Signs involving central (e.g. hallucinations, confusion, amnesia, myoclonus), autonomic (e.g. variations in blood pressure, hyperhidrosis) and peripheral (e.g. painful cramps, myokymia) hyperactivity, as well as systemic manifestations (such as weight loss, pruritus, fever), are reported. Thymoma is present in some cases. |
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| definition_citation |
Orphanet |
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| expertlink |
https://www.orpha.net/consor/cgi-bin/OC_Exp.php?Lng=en&Expert=83467 |
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| has_age_of_onset |
Adult |
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| hasDbXref |
ICD-10:G60.8 ICD-11:8E4A.3 MedDRA:10075006 UMLS:C3854373 |
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| label |
Morvan syndrome |
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| notation |
ORPHA:83467 |
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| part_of |
http://www.orpha.net/ORDO/Orphanet_221114 |
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| prefixIRI |
ORDO:Orphanet_83467 |
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| prefLabel |
Morvan syndrome |
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| present_in |
Worldwide AND has_cases/families_value : 60.0 (Case) Worldwide AND has_point_prevalence_range : <1 / 1 000 000 |
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| treeView |
http://www.orpha.net/ORDO/Orphanet_221114 |
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| subClassOf |