Orphanet Rare Disease Ontology

Last uploaded: July 3, 2024
Preferred Name

Non-histaminic angioedema

Synonyms

Non histamine-induced angioedema

Bradykinine-induced angioedema

Angioneurotic edema

Definitions

A disorder that is characterized by the occurrence of transitory and recurrent subcutaneous and/or submucosal edemas resulting in swelling and/or abdominal pain.

ID

http://www.orpha.net/ORDO/Orphanet_658

alternative_term

Non histamine-induced angioedema

Bradykinine-induced angioedema

Angioneurotic edema

definition

A disorder that is characterized by the occurrence of transitory and recurrent subcutaneous and/or submucosal edemas resulting in swelling and/or abdominal pain.

definition_citation

Orphanet

expertlink

https://www.orpha.net/consor/cgi-bin/OC_Exp.php?Lng=en&Expert=658

has_age_of_onset

All ages

has_inheritance

Not applicable

Autosomal dominant

label

Non-histaminic angioedema

notation

Clinical group

ORPHA:658

prefixIRI

ORDO:Orphanet_658

prefLabel

Non-histaminic angioedema

present_in

Europe AND has_point_prevalence_range : 1-9 / 100 000

subClassOf

http://www.orpha.net/ORDO/Orphanet_98050

http://www.orpha.net/ORDO/Orphanet_98023

http://www.orpha.net/ORDO/Orphanet_557492

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