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Orphanet Rare Disease Ontology
Last uploaded:
December 4, 2024
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| Id | http://www.orpha.net/ORDO/Orphanet_611
http://www.orpha.net/ORDO/Orphanet_611
|
|---|---|
| Preferred Name | Inclusion body myositis |
| Definitions |
A rare degenerative inflammatory disorder of skeletal muscles characterized by late onset weakness, starting in either the quadriceps or finger flexors and slowly progressing to include other groups of limb muscles. Distinctive histopathological features include inflammatory and degenerative features.
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| Synonyms |
IBM
Sporadic inclusion body myositis
sIBM
|
| Type | http://www.w3.org/2002/07/owl#Class |
All Properties
| definition_citation | Orphanet |
|---|---|
| definition | A rare degenerative inflammatory disorder of skeletal muscles characterized by late onset weakness, starting in either the quadriceps or finger flexors and slowly progressing to include other groups of limb muscles. Distinctive histopathological features include inflammatory and degenerative features. |
| label |
Inclusion body myositis
|
| prefLabel |
Inclusion body myositis
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| hasDbXref |
MedDRA:10066407
ICD-10:M60.8
ICD-11:4A41.20
OMIM:147421
MeSH:D018979
UMLS:C0238190
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|
| notation |
ORPHA:611
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| alternative_term |
IBM
Sporadic inclusion body myositis
sIBM
|
| present_in |
United States AND has_point_prevalence_average_value : 1.1 AND has_point_prevalence_range : 1-9 / 100 000
Sweden AND has_point_prevalence_average_value : 3.2 AND has_point_prevalence_range : 1-9 / 100 000
Netherlands AND has_point_prevalence_average_value : 0.49 AND has_point_prevalence_range : 1-9 / 1 000 000
Sweden AND has_annual_incidence_average_value : 2.5 AND has_annual_incidence_range : 1-9 / 1 000 000
Australia AND has_point_prevalence_average_value : 1.2 AND has_point_prevalence_range : 1-9 / 100 000
Turkey AND has_point_prevalence_average_value : 0.1 AND has_point_prevalence_range : 1-9 / 1 000 000
Europe AND has_point_prevalence_average_value : 0.5 AND has_point_prevalence_range : 1-9 / 1 000 000
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| part_of | |
| prefixIRI |
ORDO:Orphanet_611
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| expertlink | |
| subClassOf | |
| type | |
| has_inheritance |
Not applicable
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| has_age_of_onset |
Adult
Elderly
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