Preferred Name |
Inclusion body myositis |
|
Synonyms |
IBM |
|
Definitions |
A rare degenerative inflammatory disorder of skeletal muscles characterized by late onset weakness, starting in either the quadriceps or finger flexors and slowly progressing to include other groups of limb muscles. Distinctive histopathological features include inflammatory and degenerative features. |
|
ID |
http://www.orpha.net/ORDO/Orphanet_611 |
|
alternative_term |
IBM Sporadic inclusion body myositis sIBM |
|
definition |
A rare degenerative inflammatory disorder of skeletal muscles characterized by late onset weakness, starting in either the quadriceps or finger flexors and slowly progressing to include other groups of limb muscles. Distinctive histopathological features include inflammatory and degenerative features. |
|
definition_citation |
Orphanet |
|
expertlink |
https://www.orpha.net/consor/cgi-bin/OC_Exp.php?lng=en&Expert=611 |
|
has_age_of_onset |
Adult Elderly |
|
has_inheritance |
Not applicable |
|
hasDbXref |
MedDRA:10066407 ICD-10:M60.8 ICD-11:4A41.20 OMIM:147421 MeSH:D018979 UMLS:C0238190 |
|
label |
Inclusion body myositis |
|
notation |
ORPHA:611 |
|
part_of | ||
prefixIRI |
ORDO:Orphanet_611 |
|
prefLabel |
Inclusion body myositis |
|
present_in |
United States AND has_point_prevalence_average_value : 1.1 AND has_point_prevalence_range : 1-9 / 100 000 Sweden AND has_point_prevalence_average_value : 3.2 AND has_point_prevalence_range : 1-9 / 100 000 Netherlands AND has_point_prevalence_average_value : 0.49 AND has_point_prevalence_range : 1-9 / 1 000 000 Sweden AND has_annual_incidence_average_value : 2.5 AND has_annual_incidence_range : 1-9 / 1 000 000 Australia AND has_point_prevalence_average_value : 1.2 AND has_point_prevalence_range : 1-9 / 100 000 Turkey AND has_point_prevalence_average_value : 0.1 AND has_point_prevalence_range : 1-9 / 1 000 000 Europe AND has_point_prevalence_average_value : 0.5 AND has_point_prevalence_range : 1-9 / 1 000 000 |
|
treeView | ||
subClassOf |