Orphanet Rare Disease Ontology

Last uploaded: December 13, 2023
Preferred Name

Classic Hodgkin lymphoma

Synonyms

Classic Hodgkin disease

Definitions

Classical Hodgkin lymphoma (CHL) is a B-cell lymphoma characterized histologically by the presence of large mononuclear Hodgkin cells and multinucleated Reed-Sternberg (HRS) cells.

ID

http://www.orpha.net/ORDO/Orphanet_391

alternative_term

Classic Hodgkin disease

definition

Classical Hodgkin lymphoma (CHL) is a B-cell lymphoma characterized histologically by the presence of large mononuclear Hodgkin cells and multinucleated Reed-Sternberg (HRS) cells.

definition_citation

Orphanet

expertlink

https://www.orpha.net/consor/cgi-bin/OC_Exp.php?lng=en&Expert=391

has_age_of_onset

All ages

has_inheritance

Unknown

hasDbXref

ICD-10:C81.9

UMLS:C1333064

ICD-10:C81.2

ICD-10:C81.0

ICD-10:C81.3

ICD-10:C81.7

ICD-10:C81.1

OMIM:236000

OMIM:300221

ICD-11:2B30.1

ICD-10:C81.4

OMIM:400021

label

Classic Hodgkin lymphoma

notation

ORPHA:391

part_of

http://www.orpha.net/ORDO/Orphanet_98293

prefixIRI

ORDO:Orphanet_391

prefLabel

Classic Hodgkin lymphoma

present_in

Portugal AND has_annual_incidence_average_value : 2.435 AND has_annual_incidence_range : 1-9 / 100 000

Germany AND has_annual_incidence_average_value : 2.333 AND has_annual_incidence_range : 1-9 / 100 000

Switzerland AND has_annual_incidence_average_value : 3.091 AND has_annual_incidence_range : 1-9 / 100 000

Croatia AND has_annual_incidence_average_value : 2.923 AND has_annual_incidence_range : 1-9 / 100 000

Ireland AND has_annual_incidence_average_value : 2.355 AND has_annual_incidence_range : 1-9 / 100 000

Belgium AND has_annual_incidence_average_value : 2.443 AND has_annual_incidence_range : 1-9 / 100 000

Iceland AND has_annual_incidence_average_value : 2.599 AND has_annual_incidence_range : 1-9 / 100 000

Finland AND has_annual_incidence_average_value : 2.232 AND has_annual_incidence_range : 1-9 / 100 000

Estonia AND has_annual_incidence_average_value : 2.392 AND has_annual_incidence_range : 1-9 / 100 000

Latvia AND has_annual_incidence_average_value : 1.868 AND has_annual_incidence_range : 1-9 / 100 000

Europe AND has_annual_incidence_average_value : 2.463 AND has_annual_incidence_range : 1-9 / 100 000

United States AND has_annual_incidence_average_value : 2.8 AND has_annual_incidence_range : 1-9 / 100 000

Czech Republic AND has_annual_incidence_average_value : 2.418 AND has_annual_incidence_range : 1-9 / 100 000

Spain AND has_annual_incidence_average_value : 2.617 AND has_annual_incidence_range : 1-9 / 100 000

Slovakia AND has_annual_incidence_average_value : 2.261 AND has_annual_incidence_range : 1-9 / 100 000

United Kingdom AND has_annual_incidence_average_value : 2.504 AND has_annual_incidence_range : 1-9 / 100 000

France AND has_annual_incidence_average_value : 2.95 AND has_annual_incidence_range : 1-9 / 100 000

China AND has_annual_incidence_average_value : 0.25 AND has_annual_incidence_range : 1-9 / 1 000 000

Japan AND has_annual_incidence_average_value : 0.25 AND has_annual_incidence_range : 1-9 / 1 000 000

Bulgaria AND has_annual_incidence_average_value : 2.083 AND has_annual_incidence_range : 1-9 / 100 000

Italy AND has_annual_incidence_average_value : 3.361 AND has_annual_incidence_range : 1-9 / 100 000

Malta AND has_annual_incidence_average_value : 2.701 AND has_annual_incidence_range : 1-9 / 100 000

Norway AND has_annual_incidence_average_value : 2.267 AND has_annual_incidence_range : 1-9 / 100 000

Poland AND has_annual_incidence_average_value : 2.2 AND has_annual_incidence_range : 1-9 / 100 000

Slovenia AND has_annual_incidence_average_value : 2.265 AND has_annual_incidence_range : 1-9 / 100 000

Lithuania AND has_annual_incidence_average_value : 2.372 AND has_annual_incidence_range : 1-9 / 100 000

Netherlands AND has_annual_incidence_average_value : 2.27 AND has_annual_incidence_range : 1-9 / 100 000

Austria AND has_annual_incidence_average_value : 2.012 AND has_annual_incidence_range : 1-9 / 100 000

Europe AND has_lifetime_prevalence_average_value : 22.9 AND has_lifetime_prevalence_range : 1-5 / 10 000

Europe AND has_point_prevalence_range : 1-5 / 10 000

treeView

http://www.orpha.net/ORDO/Orphanet_98293

subClassOf

http://www.orpha.net/ORDO/Orphanet_377788

http://www.orpha.net/ORDO/Orphanet_557493

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